Atypical presentation of Rosai-Dorfman disease in the lacrimal gland mimicking malignancy.

A 29-year-old man presented with a painful, rapidly growing mass in the right upper eyelid. Ophthalmic and systemic examinations and results of laboratory investigations were all normal. CT revealed a mass in the right lacrimal region with surrounding bone destruction, which was suggestive of a malignant lacrimal gland tumor. Histologic analysis of the biopsy specimen supported a diagnosis of Rosai-Dorfman disease with no lymphadenopathy.