Literature DB >> 16502301

LED-generated multifocal ERG on- and off-responses in complete congenital stationary night blindness -- a case report.

Dorothee Leifert1, Margarita G Todorova, Chrisitan Prünte, Anja M Palmowski-Wolfe.   

Abstract

We report on the application of a light emitting diode (LED) screen to elicit multifocal ERG on- and off-responses in a patient presenting with the complete type of congenital stationary night blindness (cCSNB): A 63-years old woman was diagnosed with cCSNB by means of standard ERG procedures and dark adaptometry. To confirm this diagnosis and to investigate topographical differences of on- and off-responses a multifocal approach employing long-duration stimuli was added. Results of mfERG-testing were averaged in three groups (a central area of 7.5 degrees , a ring area of 7.5-21.9 degrees and a peripheral ring of 21.9-31.1 degrees ). When compared to normal controls (n = 4) on-responses (P1-amplitudes) were severely reduced symmetrically at all eccentricities, while off-responses showed no reduction resulting in an increased off/on-ratio. Furthermore on-latencies of P1 were delayed symmetrically at all eccentricities, whereas off-latencies were normal. To our knowledge this is the first report of multifocal on- and off-responses in a CSNB-patient. Stimulus-generation with a LED-screen provides the advantage of a stable luminance during the long-duration on-phase.

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Year:  2006        PMID: 16502301     DOI: 10.1007/s10633-005-2303-1

Source DB:  PubMed          Journal:  Doc Ophthalmol        ISSN: 0012-4486            Impact factor:   2.379


  12 in total

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4.  Autosomal dominant stationary night-blindness. A large family rediscovered.

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5.  Congenital stationary night blindness with negative electroretinogram. A new classification.

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7.  The complete form of X-linked congenital stationary night blindness is caused by mutations in a gene encoding a leucine-rich repeat protein.

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8.  Mutations in NYX, encoding the leucine-rich proteoglycan nyctalopin, cause X-linked complete congenital stationary night blindness.

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9.  A novel CACNA1F mutation in a french family with the incomplete type of X-linked congenital stationary night blindness.

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10.  Rod and cone function in the Nougaret form of stationary night blindness.

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  1 in total

1.  Gradient of deficit in cone responses in the incomplete form of congenital stationary night blindness revealed by multifocal electroretinography.

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  1 in total

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