| Literature DB >> 16501881 |
M A Hamdan1, R M Abu-Sulaiman, H K Najm.
Abstract
Unilateral agenesis of the pulmonary artery (PA) is a rare anomaly that can lead to pulmonary hypertension (PHTN). We report the case of a 10-month-old female with agenesis of the left PA, ventricular septal defect, and patent ductus arteriosus who developed PHTN precluding surgical repair. The use of sildenafil decreased PA pressure and normalized pulmonary vascular resistance, after which surgery was successfully performed.Entities:
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Year: 2006 PMID: 16501881 DOI: 10.1007/s00246-005-1100-7
Source DB: PubMed Journal: Pediatr Cardiol ISSN: 0172-0643 Impact factor: 1.655