| Literature DB >> 16376794 |
Nanda Kerkar1, Karen Norton, Frederick J Suchy.
Abstract
The hepatic fibrocystic diseases present with variable intrahepatic biliary abnormalities, which range from portal tract enlargement and fibrosis to cystic formations. They may present as autosomal recessive or dominant polycystic kidney diseases, with associated dilatation of the renal collecting system, or as incompletely characterized cystic diseases. Symptoms from the liver disease often result from complications of fibrosis or dilated ducts/cyst (sludge, lithiasis, infection). The treatment is supportive, with careful attention to associated renal disease. Liver transplantation is an option in selected patients.Entities:
Mesh：
Year: 2006 PMID： 16376794 DOI： 10.1016/j.cld.2005.10.003
Source DB: PubMed Journal: Clin Liver Dis ISSN： 1089-3261 Impact factor: 6.126