Literature DB >> 16359978

Reversibility of hypogonadotropic hypogonadism in a patient with the juvenile form of hemochromatosis.

Nicholas G Angelopoulos1, Anastasia Goula, Evagelos Dimitriou, George Tolis.   

Abstract

OBJECTIVE: To report a case of complete reversibility of hypogonadotropic hypogonadism with intensive venesection treatment in juvenile hemochromatosis.
DESIGN: Case report.
SETTING: Endocrine department of Hippocrateion Hospital of Athens. PATIENT(S): A 25-year-old man who presented with hypogonadotropic hypogonadism and severe iron overload due to juvenile hemochromatosis and who was initially treated with phlebotomies and androgen substitution. INTERVENTION(S): Intensification of chelation therapy. MAIN OUTCOME MEASURE(S): Clinical evaluation, serum ferritin concentration, and biochemical assessment of pituitary function were performed periodically. RESULT(S): One year after normalization of serum ferritin levels and transferrin saturation was achieved, he became eugonadal. CONCLUSION(S): We believe that hypogonadotropic hypogonadism in juvenile hemochromatosis may be reversible by a consequent venesection therapy probably because treatment was intensive and promptly introduced at a young age.

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Year:  2005        PMID: 16359978     DOI: 10.1016/j.fertnstert.2005.05.070

Source DB:  PubMed          Journal:  Fertil Steril        ISSN: 0015-0282            Impact factor:   7.329


  3 in total

1.  Iron Overload (with Attention to Genetic Testing and Diagnosis/Management of HFE Wild Type Patients).

Authors:  Narendra Siddaiah; Kris V Kowdley
Journal:  Curr Treat Options Gastroenterol       Date:  2006

Review 2.  Genotypic and phenotypic spectra of hemojuvelin mutations in primary hemochromatosis patients: a systematic review.

Authors:  Xiaomu Kong; Lingding Xie; Haiqing Zhu; Lulu Song; Xiaoyan Xing; Wenying Yang; Xiaoping Chen
Journal:  Orphanet J Rare Dis       Date:  2019-07-08       Impact factor: 4.123

Review 3.  Current National and International Guidelines for the Management of Male Hypogonadism: Helping Clinicians to Navigate Variation in Diagnostic Criteria and Treatment Recommendations.

Authors:  Ahmed Al-Sharefi; Richard Quinton
Journal:  Endocrinol Metab (Seoul)       Date:  2020-09-22
  3 in total

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