Literature DB >> 16314243

Extramedullary hematopoiesis with spinal cord compression in beta-thalassemia intermedia.

Massoud Saghafi1, Abbas Shirdel, Shahrzad M Lari.   

Abstract

Spinal cord compression due to extramedullary hematopoiesis is a rare manifestation of thalassemia. We present a 28-year-old woman with beta-thalassemia intermedia and progressive paraparesis. She had a thoracic extradural extramedullary mass lesion on MRI. She improved after receiving multiple transfusions. Clinical awareness of this phenomenon with early treatment is essential for a successful outcome.

Entities:  

Year:  2005        PMID: 16314243     DOI: 10.1016/j.ejim.2005.04.010

Source DB:  PubMed          Journal:  Eur J Intern Med        ISSN: 0953-6205            Impact factor:   4.487


  4 in total

1.  Chronic idiopathic myelofibrosis presenting as cauda equina compression due to extramedullary hematopoiesis: a case report.

Authors:  Duck Ho Goh; Sun Ho Lee; Dae Chul Cho; Seong Hyun Park; Jeong Hyun Hwang; Joo Kyung Sung
Journal:  J Korean Med Sci       Date:  2007-12       Impact factor: 2.153

2.  Extramedullary hematopoiesis presenting as a right adrenal mass in a patient with Beta thalassemia.

Authors:  Hossein Karami; Mehrnoush Kosaryan; Mehrdad Taghipour; Rayka Sharifian; Aili Aliasgharian; Mohsen Motalebi
Journal:  Nephrourol Mon       Date:  2014-09-05

3.  Adrenal extramedullary hematopoiesis associated with beta-thalassemia trait in an adult woman: a case report and review of literature.

Authors:  Hassan Al-Thani; Maryam Al-Sulaiti; Gamela El-Mabrok; AbdelHakim Tabeb; Ayman El-Menyar
Journal:  Int J Surg Case Rep       Date:  2016-05-19

4.  Extramedullary hematopoiesis presented as cytopenia and massive paraspinal masses leading to cord compression in a patient with hereditary persistence of fetal hemoglobin.

Authors:  Tasleem Katchi; Krishna Kolandaivel; Pallavi Khattar; Taliya Farooq; Humayun Islam; Delong Liu
Journal:  Biomark Res       Date:  2016-09-01
  4 in total

北京卡尤迪生物科技股份有限公司 © 2022-2023.