Literature DB >> 161495

[Papillon-Lefèvre syndrome and recurrent infections].

M H Marandian, N Foroozanfar, H Haghigat, S Saket, M Lessani, M Djafarian.   

Abstract

Seven cases of Papillon-Lefevre syndrome are described, 4 children and their mother with two other relatives on the mother's side. An immune defect was suspected because six of the seven had a history of severe pyogenic infections, but the results of the tests were not the same in the three individuals tested. In one patient no immune defect was detected but in the other two the response of lymphocytes to candida and to streptokinase and streptodornase was reduced.

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Year:  1979        PMID: 161495

Source DB:  PubMed          Journal:  Arch Fr Pediatr        ISSN: 0003-9764


  2 in total

1.  Pyogenic liver abscess and peritonitis due to Rhizopus oryzae in a child with Papillon-Lefevre syndrome.

Authors:  Buket Dalgic; Aysegul Bukulmez; Sinan Sari
Journal:  Eur J Pediatr       Date:  2010-12-17       Impact factor: 3.183

Review 2.  Infections in patients with inherited defects in phagocytic function.

Authors:  Timothy Andrews; Kathleen E Sullivan
Journal:  Clin Microbiol Rev       Date:  2003-10       Impact factor: 26.132

  2 in total

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