Literature DB >> 16126046

Biliary atresia: clinical profiles, risk factors, and outcomes of 755 patients listed for liver transplantation.

Elizabeth C Utterson1, Ross W Shepherd, Ronald J Sokol, John Bucuvalas, John C Magee, Susan V McDiarmid, Ravinder Anand.   

Abstract

OBJECTIVES: To test the hypothesis that risk analysis from the time of listing for liver transplantation (LT) focuses attention on areas where outcomes can be improved. STUDY
DESIGN: Competing outcomes and multivariate models were used to determine significant risk factors for pretransplantation and posttransplantation mortality and graft failure in patients with biliary atresia (BA) listed for LT and enrolled in the Studies of Pediatric Liver Transplantation (SPLIT) registry.
RESULTS: Of 755 patients, most were infants (age < 1 year). Significant waiting list mortality risk factors included infancy and pediatric end-stage liver disease (PELD) score > or = 20, whose components were also continuous risk factors. Survival posttransplantation (n=567) was 88% at 3 years. Most deaths were from infection (37%). Posttransplantation mortality risk factors included infant recipients, height/weight < -2 standard deviations (SD), use of cyclosporine versus tacrolimus and retransplantation. Graft failure risks included height/weight < -2 SD, cadaveric partial donors, donor age < or = 5 months, use of cyclosporine versus tacrolimus, and rejection.
CONCLUSIONS: Referral for LT should be anticipatory for infants with BA with failed portoenterostomies. Failing nutrition should prompt aggressive support. Post-LT risk factors are mainly nonsurgical, including nutrition, the relative risk of infection over rejection, and the choice of immunosuppression.

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Year:  2005        PMID: 16126046     DOI: 10.1016/j.jpeds.2005.04.073

Source DB:  PubMed          Journal:  J Pediatr        ISSN: 0022-3476            Impact factor:   4.406


  40 in total

1.  Does the pediatric end-stage liver disease score or hepatic artery resistance index predict outcome after liver transplantation for biliary atresia?

Authors:  Sonal Asthana; Patricia McClean; Mark D Stringer
Journal:  Pediatr Surg Int       Date:  2006-08-01       Impact factor: 1.827

2.  The outcome of laparoscopic portoenterostomy for biliary atresia in children.

Authors:  Kin Wai Edwin Chan; Kim Hung Lee; Jennifer Wai Cheung Mou; Sing Tak Gloria Cheung; Yuk Him Peter Tam
Journal:  Pediatr Surg Int       Date:  2011-02-01       Impact factor: 1.827

3.  Long-term results of biliary atresia in the era of liver transplantation.

Authors:  Sanghoon Lee; Hyojun Park; Suk-Bae Moon; Soo-Min Jung; Jong Man Kim; Choon Hyuck David Kwon; Sung Joo Kim; Jae-Won Joh; Jeong-Meen Seo; Suk-Koo Lee
Journal:  Pediatr Surg Int       Date:  2013-08-15       Impact factor: 1.827

4.  Parenteral nutrition supplementation in biliary atresia patients listed for liver transplantation.

Authors:  Jillian S Sullivan; Shikha S Sundaram; Zhaoxing Pan; Ronald J Sokol
Journal:  Liver Transpl       Date:  2012-01       Impact factor: 5.799

5.  A 10-Year united network for organ sharing review of mortality and risk factors in young children awaiting liver transplantation.

Authors:  Daniel H Leung; Amrita Narang; Charles G Minard; Girish Hiremath; John A Goss; Ross Shepherd
Journal:  Liver Transpl       Date:  2016-11       Impact factor: 5.799

6.  Impact of the Pediatric End-Stage Liver Disease (PELD) growth failure thresholds on mortality among pediatric liver transplant candidates.

Authors:  Sonja M Swenson; John P Roberts; Sue Rhee; Emily R Perito
Journal:  Am J Transplant       Date:  2019-09-03       Impact factor: 8.086

Review 7.  Recent developments in diagnostics and treatment of neonatal cholestasis.

Authors:  Amy G Feldman; Ronald J Sokol
Journal:  Semin Pediatr Surg       Date:  2020-07-23       Impact factor: 2.754

8.  Risk factors for rejection and infection in pediatric liver transplantation.

Authors:  R W Shepherd; Y Turmelle; M Nadler; J A Lowell; M R Narkewicz; S V McDiarmid; R Anand; C Song
Journal:  Am J Transplant       Date:  2007-12-19       Impact factor: 8.086

9.  Reducing pediatric liver transplant complications: a potential roadmap for transplant quality improvement initiatives within North America.

Authors:  M J Englesbe; B Kelly; J Goss; A Fecteau; J Mitchell; W Andrews; G Krapohl; J C Magee; G Mazariegos; S Horslen; J Bucuvalas
Journal:  Am J Transplant       Date:  2012-08-06       Impact factor: 8.086

10.  Biliary atresia.

Authors:  C K Sinha; Mark Davenport
Journal:  J Indian Assoc Pediatr Surg       Date:  2008-04
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