Case report: clinical and radiological features of Cogan's syndrome--non-syphilitic interstitial keratitis, audiovestibular symptoms and systemic manifestations.

The case is presented of a 23-year-old man with Cogan's syndrome, who died from spontaneous rupture of a renal artery 2 years after developing symptoms, despite treatment with corticosteroids and azathioprine. The typical clinical features, investigations and radiological findings of this rare disease are described, particularly the systemic vasculitis and its angiographic and ultrasound appearances.