Literature DB >> 16024850

Gorlin syndrome: the PTCH gene links ocular developmental defects and tumour formation.

N K Ragge1, A Salt, J R O Collin, A Michalski, P A Farndon.   

Abstract

AIM: To identify a gene linking microphthalmia with cyst with early onset medulloblastoma.
METHODS: Mutation analysis of the PTCH gene.
RESULTS: A mutation in exon 10 of the PTCH gene was identified, confirming a diagnosis of Gorlin syndrome.
CONCLUSIONS: This is the first genetically identified mutation giving rise to microphthalmia with cyst and provides a valuable link in the eye developmental gene pathway.

Entities:  

Mesh:

Substances:

Year:  2005        PMID: 16024850      PMCID: PMC1772759          DOI: 10.1136/bjo.2004.061390

Source DB:  PubMed          Journal:  Br J Ophthalmol        ISSN: 0007-1161            Impact factor:   4.638


  29 in total

Review 1.  The sonic hedgehog-patched-gli pathway in human development and disease.

Authors:  E H Villavicencio; D O Walterhouse; P M Iannaccone
Journal:  Am J Hum Genet       Date:  2000-09-21       Impact factor: 11.025

2.  Prediction of central nervous system embryonal tumour outcome based on gene expression.

Authors:  Scott L Pomeroy; Pablo Tamayo; Michelle Gaasenbeek; Lisa M Sturla; Michael Angelo; Margaret E McLaughlin; John Y H Kim; Liliana C Goumnerova; Peter M Black; Ching Lau; Jeffrey C Allen; David Zagzag; James M Olson; Tom Curran; Cynthia Wetmore; Jaclyn A Biegel; Tomaso Poggio; Shayan Mukherjee; Ryan Rifkin; Andrea Califano; Gustavo Stolovitzky; David N Louis; Jill P Mesirov; Eric S Lander; Todd R Golub
Journal:  Nature       Date:  2002-01-24       Impact factor: 49.962

3.  Cloning and molecular characterization of a metabolic gene with development functions in Drosophila. I. Analysis of the head function of Punch.

Authors:  J R McLean; R Boswell; J O'Donnell
Journal:  Genetics       Date:  1990-12       Impact factor: 4.562

4.  CHX10 mutations cause non-syndromic microphthalmia/ anophthalmia in Arab and Jewish kindreds.

Authors:  Udy Bar-Yosef; Izzeldin Abuelaish; Tamar Harel; Neta Hendler; Rivka Ofir; Ohad S Birk
Journal:  Hum Genet       Date:  2004-09       Impact factor: 4.132

5.  Abnormalities of the vitreoretinal interface caused by dysregulated Hedgehog signaling during retinal development.

Authors:  Graeme C M Black; Chantal J Mazerolle; Yaping Wang; Katrina D Campsall; Dino Petrin; Brian C Leonard; Karim F Damji; D Gareth Evans; David McLeod; Valerie A Wallace
Journal:  Hum Mol Genet       Date:  2003-10-21       Impact factor: 6.150

6.  Molecular screening of SHH, ZIC2, SIX3, and TGIF genes in patients with features of holoprosencephaly spectrum: Mutation review and genotype-phenotype correlations.

Authors:  Christèle Dubourg; Leïla Lazaro; Laurent Pasquier; Claude Bendavid; Martine Blayau; Franck Le Duff; Marie-Renée Durou; Sylvie Odent; Véronique David
Journal:  Hum Mutat       Date:  2004-07       Impact factor: 4.878

7.  Mutation and cancer: statistical study of retinoblastoma.

Authors:  A G Knudson
Journal:  Proc Natl Acad Sci U S A       Date:  1971-04       Impact factor: 11.205

8.  The management of orbital cysts associated with congenital microphthalmos and anophthalmos.

Authors:  C J McLean; N K Ragge; R B Jones; J R O Collin
Journal:  Br J Ophthalmol       Date:  2003-07       Impact factor: 4.638

9.  Novel mutation in sonic hedgehog in non-syndromic colobomatous microphthalmia.

Authors:  Lisa A Schimmenti; June de la Cruz; Richard Alan Lewis; J D Karkera; Glenda S Manligas; Erich Roessler; Maximilian Muenke
Journal:  Am J Med Genet A       Date:  2003-01-30       Impact factor: 2.802

10.  Microphthalmos with cyst in monozygous twins.

Authors:  B Leatherbarrow; J Kwartz; J L Noble
Journal:  J Pediatr Ophthalmol Strabismus       Date:  1990 Nov-Dec       Impact factor: 1.402

View more
  14 in total

1.  Gorlin syndrome and bilateral ovarian fibroma.

Authors:  Fernanda Pirschner; Pollyana Marçal Bastos; George Luiz Contarato; Anna Carolina Bon Lima Bimbato; Antônio Chambô Filho
Journal:  Int J Surg Case Rep       Date:  2012-06-02

2.  Multisystem Involvement in a Patient with a PTCH1 Mutation: Clinical and Imaging Findings.

Authors:  Antonio Richieri-Costa; Siulan Vendramini-Pittoli; Nancy Mizue Kokitsu-Nakata; Roseli Maria Zechi-Ceide; Camila Wenceslau Alvarez; Lucilene Arilho Ribeiro-Bicudo
Journal:  J Pediatr Genet       Date:  2016-09-14

3.  Correlation and expression of COX-2 and P53 protein in basal cell carcinoma of eyelid.

Authors:  Zhixiong Chen; Jiong Yang; Qiong Huang
Journal:  J Huazhong Univ Sci Technolog Med Sci       Date:  2009-06-10

4.  SOX2 anophthalmia syndrome: 12 new cases demonstrating broader phenotype and high frequency of large gene deletions.

Authors:  P Bakrania; D O Robinson; D J Bunyan; A Salt; A Martin; J A Crolla; A Wyatt; A Fielder; J Ainsworth; A Moore; S Read; J Uddin; D Laws; D Pascuel-Salcedo; C Ayuso; L Allen; J R O Collin; N K Ragge
Journal:  Br J Ophthalmol       Date:  2007-05-23       Impact factor: 4.638

Review 5.  Genetics of anophthalmia and microphthalmia. Part 2: Syndromes associated with anophthalmia-microphthalmia.

Authors:  Anne Slavotinek
Journal:  Hum Genet       Date:  2018-10-30       Impact factor: 4.132

Review 6.  Review of Ocular Manifestations of Nevoid Basal Cell Carcinoma Syndrome: What an Ophthalmologist Needs to Know.

Authors:  Judy J Chen; Juliana Sartori; Vinay K Aakalu; Pete Setabutr
Journal:  Middle East Afr J Ophthalmol       Date:  2015 Oct-Dec

7.  Activation of Sonic hedgehog signaling in neural progenitor cells promotes glioma development in the zebrafish optic pathway.

Authors:  B Ju; W Chen; J M Spitsbergen; J Lu; P Vogel; J L Peters; Y-D Wang; B A Orr; J Wu; H E Henson; S Jia; C Parupalli; M R Taylor
Journal:  Oncogenesis       Date:  2014-03-31       Impact factor: 7.485

8.  A role for smoothened during murine lens and cornea development.

Authors:  Janet J Y Choi; Chao-Tung Ting; Lidia Trogrlic; Stefan V Milevski; Mary Familari; Gemma Martinez; Robb U de Iongh
Journal:  PLoS One       Date:  2014-09-30       Impact factor: 3.240

9.  Targeted resequencing identifies PTCH1 as a major contributor to ocular developmental anomalies and extends the SOX2 regulatory network.

Authors:  Nicolas Chassaing; Erica E Davis; Kelly L McKnight; Adrienne R Niederriter; Alexandre Causse; Véronique David; Annaïck Desmaison; Sophie Lamarre; Catherine Vincent-Delorme; Laurent Pasquier; Christine Coubes; Didier Lacombe; Massimiliano Rossi; Jean-Louis Dufier; Helene Dollfus; Josseline Kaplan; Nicholas Katsanis; Heather C Etchevers; Stanislas Faguer; Patrick Calvas
Journal:  Genome Res       Date:  2016-02-18       Impact factor: 9.043

10.  Mutations in BMP4 cause eye, brain, and digit developmental anomalies: overlap between the BMP4 and hedgehog signaling pathways.

Authors:  Preeti Bakrania; Maria Efthymiou; Johannes C Klein; Alison Salt; David J Bunyan; Alex Wyatt; Chris P Ponting; Angela Martin; Steven Williams; Victoria Lindley; Joanne Gilmore; Marie Restori; Anthony G Robson; Magella M Neveu; Graham E Holder; J Richard O Collin; David O Robinson; Peter Farndon; Heidi Johansen-Berg; Dianne Gerrelli; Nicola K Ragge
Journal:  Am J Hum Genet       Date:  2008-01-31       Impact factor: 11.025

View more

北京卡尤迪生物科技股份有限公司 © 2022-2023.