| Literature DB >> 15957181 |
Soraisham Amuchou Singh1, Thowfique Ibrahim, Deborah Jane Clark, Richard Scott Taylor, David Hilles George.
Abstract
Congenital alveolar capillary dysplasia is a rare and fatal cause of pulmonary hypertension in neonates. We report on a term baby with severe pulmonary hypertension unresponsive to high-frequency ventilation and nitric oxide. A diagnosis of alveolar capillary dysplasia was established on autopsy. We review the literature regarding pathophysiology, clinical presentations, associated malformations, and treatment trials. 2005 Wiley-Liss, Inc.Entities:
Mesh:
Year: 2005 PMID: 15957181 DOI: 10.1002/ppul.20244
Source DB: PubMed Journal: Pediatr Pulmonol ISSN: 1099-0496