Literature DB >> 15817096

The Brugada ECG pattern in a neonate.

Shubhayan Sanatani1, Nawal Mahkseed, Hilary Vallance, Ramon Brugada.   

Abstract

We report a neonate resuscitated from sudden death with a Brugada ECG pattern several days after the initial event. The baby was subsequently diagnosed with a fatty acid oxidation disorder (medium chain Acyl-CoA dehydrogenase deficiency or MCAD). We speculate that free fatty acid accumulation can give rise to the Brugada ECG pattern.

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Year:  2005        PMID: 15817096     DOI: 10.1046/j.1540-8167.2005.40607.x

Source DB:  PubMed          Journal:  J Cardiovasc Electrophysiol        ISSN: 1045-3873


  6 in total

Review 1.  Brugada syndrome in childhood: a potential fatal arrhythmia not always recognised by paediatricians. A case report and review of the literature.

Authors:  Yvan Mivelaz; Stefano Di Bernardo; Etienne Pruvot; Erik Jan Meijboom; Nicole Sekarski
Journal:  Eur J Pediatr       Date:  2006-05-03       Impact factor: 3.183

2.  Extracorporeal Life Support as a Rescue Measure for Managing Life-Threatening Arrythmia and Brugada Syndrome.

Authors:  Asaad G Beshish; Allison Weinberg; Waseem Ostwani; Gabe E Owens
Journal:  J Extra Corpor Technol       Date:  2017-12

Review 3.  Prolonged QTc interval in association with medium-chain acyl-coenzyme A dehydrogenase deficiency.

Authors:  Jason R Wiles; Nancy Leslie; Timothy K Knilans; Henry Akinbi
Journal:  Pediatrics       Date:  2014-05-05       Impact factor: 7.124

Review 4.  Brugada syndrome.

Authors:  Charles Antzelevitch
Journal:  Pacing Clin Electrophysiol       Date:  2006-10       Impact factor: 1.976

5.  Recurrent Ventricular Tachycardia in Medium-Chain Acyl-Coenzyme A Dehydrogenase Deficiency.

Authors:  P Bala; S Ferdinandusse; S E Olpin; P Chetcuti; A A M Morris
Journal:  JIMD Rep       Date:  2015-09-25

6.  Brugada-like syndrome in infancy presenting with rapid ventricular tachycardia and intraventricular conduction delay.

Authors:  Ronald J Kanter; Ryan Pfeiffer; Dan Hu; Héctor Barajas-Martinez; Michael P Carboni; Charles Antzelevitch
Journal:  Circulation       Date:  2011-11-16       Impact factor: 29.690

  6 in total

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