Literature DB >> 15757617

Evaluation of left ventricular dimensions and function in Marfan's syndrome without significant valvular regurgitation.

Lilian J Meijboom1, Janneke Timmermans, Johan P van Tintelen, Gijs J Nollen, Julie De Backer, Maarten P van den Berg, Gerard H Boers, Barbara J M Mulder.   

Abstract

Left ventricular dimensions and systolic function were studied using echocardiography in 234 patients with Marfan's syndrome without significant valvular regurgitation. Left ventricular dimensions and systolic function were found to be normal in most patients with Marfan's syndrome. Some involvement of the left ventricle may have been present in a small group of these patients. No patients, however, fulfilled the criteria for dilated cardiomyopathy.

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Year:  2005        PMID: 15757617     DOI: 10.1016/j.amjcard.2004.11.042

Source DB:  PubMed          Journal:  Am J Cardiol        ISSN: 0002-9149            Impact factor:   2.778


  20 in total

Review 1.  Marfan's syndrome.

Authors:  Daniel P Judge; Harry C Dietz
Journal:  Lancet       Date:  2005-12-03       Impact factor: 79.321

2.  Left atrial strain in the assessment of diastolic function: providing new insights into primary myocardial dysfunction in Marfan syndrome.

Authors:  Eusebio García-Izquierdo; Vanessa Moñivas-Palomero; Alberto Forteza; Carlos Martín-López; Mario Torres-Sanabria; Xabier Cia-Mendioroz; Consuelo Olivo-Rodríguez; Sara Navarro-Rico; Andrés Sánchez-Gómez; Jesús G Mirelis; Miguel A Cavero; Susana Mingo-Santos
Journal:  Int J Cardiovasc Imaging       Date:  2021-04-19       Impact factor: 2.357

3.  Duchenne muscular dystrophy; a cardiomyopathy that can be prevented?

Authors:  Barbara J M Mulder; Ernst E van der Wall
Journal:  Int J Cardiovasc Imaging       Date:  2008-10-01       Impact factor: 2.357

4.  Intrinsic cardiomyopathy in Marfan syndrome: results from in-vivo and ex-vivo studies of the Fbn1C1039G/+ model and longitudinal findings in humans.

Authors:  Laurence Campens; Marjolijn Renard; Bram Trachet; Patrick Segers; Laura Muino Mosquera; Johan De Sutter; Lynn Sakai; Anne De Paepe; Julie De Backer
Journal:  Pediatr Res       Date:  2015-06-04       Impact factor: 3.756

Review 5.  Marfan's syndrome and the heart.

Authors:  Alan Graham Stuart; Andrew Williams
Journal:  Arch Dis Child       Date:  2007-04       Impact factor: 3.791

Review 6.  Cardiovascular Management of Adults with Marfan Syndrome.

Authors:  Yukiko Isekame; Sabiha Gati; Jose Antonio Aragon-Martin; Rachel Bastiaenen; Sreenivasa Rao Kondapally Seshasai; Anne Child
Journal:  Eur Cardiol       Date:  2016-12

7.  Non-aortic cardiovascular disease in Marfan syndrome: a nationwide epidemiological study.

Authors:  Niels H Andersen; Kristian A Groth; Agnethe Berglund; Hanne Hove; Claus H Gravholt; Kirstine Stochholm
Journal:  Clin Res Cardiol       Date:  2021-04-22       Impact factor: 5.460

8.  Abnormal muscle mechanosignaling triggers cardiomyopathy in mice with Marfan syndrome.

Authors:  Jason R Cook; Luca Carta; Ludovic Bénard; Elie R Chemaly; Emily Chiu; Satish K Rao; Thomas G Hampton; Peter Yurchenco; Kevin D Costa; Roger J Hajjar; Francesco Ramirez
Journal:  J Clin Invest       Date:  2014-02-17       Impact factor: 14.808

9.  Nonmyocyte ERK1/2 signaling contributes to load-induced cardiomyopathy in Marfan mice.

Authors:  Rosanne Rouf; Elena Gallo MacFarlane; Eiki Takimoto; Rahul Chaudhary; Varun Nagpal; Peter P Rainer; Jay G Bindman; Elizabeth E Gerber; Djahida Bedja; Christopher Schiefer; Karen L Miller; Guangshuo Zhu; Loretha Myers; Nuria Amat-Alarcon; Dong I Lee; Norimichi Koitabashi; Daniel P Judge; David A Kass; Harry C Dietz
Journal:  JCI Insight       Date:  2017-08-03

Review 10.  Cardiovascular magnetic resonance in Marfan syndrome.

Authors:  Helen Dormand; Raad H Mohiaddin
Journal:  J Cardiovasc Magn Reson       Date:  2013-04-15       Impact factor: 5.364

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