Vasumathy Vedantham1, Kim Ramasamy. 1. Retina-Vitreous Service, Aravind Eye Hospital and Postgraduate Institute of Ophthalmology, Madurai 625 020, Tamilnadu, India. drvasumathy@yahoo.com
Abstract
PURPOSE: To report the optical coherence tomographic (OCT) findings in a case of Best's disease. DESIGN: Observational case report. METHODS: Optical coherence tomography was carried out to understand the pathogenesis of Best's disease in a 13-year-old girl. RESULTS: Optical coherence tomography demonstrated that the lipofuscin accumulated in a cystic space underneath the retinal pigment epithelium in the "pseudohypopyon stage" of Best's disease. It also demonstrated the disruption of the photoreceptors in the "scrambled egg" stage. CONCLUSIONS: These new OCT findings could explain the retention of good visual acuity in the "pseudohypopyon stage" and the loss of visual acuity in the "scrambled egg" stage of Best's disease.
PURPOSE: To report the optical coherence tomographic (OCT) findings in a case of Best's disease. DESIGN: Observational case report. METHODS: Optical coherence tomography was carried out to understand the pathogenesis of Best's disease in a 13-year-old girl. RESULTS: Optical coherence tomography demonstrated that the lipofuscin accumulated in a cystic space underneath the retinal pigment epithelium in the "pseudohypopyon stage" of Best's disease. It also demonstrated the disruption of the photoreceptors in the "scrambled egg" stage. CONCLUSIONS: These new OCT findings could explain the retention of good visual acuity in the "pseudohypopyon stage" and the loss of visual acuity in the "scrambled egg" stage of Best's disease.
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