Lymphangioma and lymphangiomyomatosis--the same lesion?

The authors present a very rare case observed in a 32 year old female with a huge tumor on the left side of the neck in which extensive changes characteristic for cystic lymphangioma in the lower part and for lymphangiomyomatosis in the upper part of the tumor were observed intraoperatively. On the basis of the discussed case the suggestion is put forward that these two rarely occurring diseases may have similar etiological grounds.