Literature DB >> 15645536

Estrogen receptors in cholangiocytes and the progression of primary biliary cirrhosis.

Domenico Alvaro1, Pietro Invernizzi, Paolo Onori, Antonio Franchitto, Adriano De Santis, Andrea Crosignani, Robert Sferra, Stefano Ginanni-Corradini, Maria Grazia Mancino, Marco Maggioni, Adolf F Attili, Mauro Podda, Eugenio Gaudio.   

Abstract

BACKGROUND/AIMS: Estrogen receptors (ER) in cholangiocytes of primary biliary cirrhosis (PBC) patients and their relationship with cell proliferation and death were evaluated.
METHODS: Liver biopsies from PBC patients with different histological stages were investigated by immunohistochemistry for ER-alpha and -beta, cytokeratin-19, proliferating cellular nuclear antigen (PCNA), Fas and terminal deoxynucleotide transferase end labelling (TUNEL). Normal livers and livers from primary sclerosing cholangitis and alcoholic cirrhosis were investigated as controls.
RESULTS: ER-alpha and -beta were observed in cholangiocytes of PBC patients but not in normal liver. In PBC, positivity for ER-beta was high (50-65 %) in all histological stages while, positivity for ER-alpha increased from 1% in stage I to 12 % in stage III (positivity correlated and co-localized in the same cell with PCNA). In stage IV of PBC, cholangiocytes were negative for ER-alpha in association with a lower PCNA positivity and with maximal degree of ductopenia. ER-alpha positivity in cholangiocytes of PBC patients was markedly lower than primary sclerosing cholangitis and alcoholic cirrhosis.
CONCLUSIONS: ER are expressed in PBC and other pathologies associated with cholangiocyte proliferation but not in normal subjects. The low expression of ER-alpha in PBC and their disappearance in the advanced histological stages suggests that an estrogenic deficiency could favour the evolution of this disease toward ductopenia.

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Year:  2004        PMID: 15645536     DOI: 10.1016/j.jhep.2004.08.022

Source DB:  PubMed          Journal:  J Hepatol        ISSN: 0168-8278            Impact factor:   25.083


  51 in total

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