| Literature DB >> 15224559 |
A Cissé1, Y Morel, M Coulibaly, I S Souaré, A F Cissé, A Nabé, L M Camara, B Cissé, S Camara, S A Bangoura, A Sylla, H Dia, L Da Silva.
Abstract
This report describes 6 cases of Wilson's disease observed at the University Hospital Center in Conakry, Guinea. Presenting symptoms involved extrapyramidal syndrome in 4 cases, psychomotor epilepsy in 1, and confusional syndrome in 1 case. Diagnosis was based on neuropsychic manifestations, Kayser-Fleicher corneal ring, liver failure, and impaired copper metabolism. Brain CT-scan depicted normal features in 3 cases, symmetric hypodensity of the lenticular nucleus in one, discrete ventricular dilatation of in one a and cortico-subcoetical atrophy in one.Entities:
Mesh:
Year: 2004 PMID: 15224559
Source DB: PubMed Journal: Med Trop (Mars) ISSN: 0025-682X