Rosai--Dorfman disease with multi-organ involvement in head and neck region.

Sinus histiocytosis with massive lymphadenopathy (Rosai-Dorfman, RD) disease is a well known entity. This pathology is differentiated from other childhood histiocytosis with its distinct features. Many sites within the head and neck area may be involved with the disease. Multi-organ involvement is very rare. A patient with Rosai-Dorfman disease involving neck, nose and larynx is presented and clinical follow-up is given.