| Literature DB >> 1488977 |
G Medina-Escobedo1, E Lopez-Corella.
Abstract
Sling left pulmonary artery (SLPA) is often associated with tracheobronchial abnormalities, including bridging bronchus (BB). We report on 3 patients with SLPA: One patient had a narrow trachea, absent right upper lobe and right main bronchus, and BB. The second patient had a long and narrow trachea, with normal segmentation of bronchial tree, abnormal cerebral gyri, and minor facial abnormalities. The third patient, with a normal trachea and main bronchi with BB, had imperforate anus, hemivertebrae, and atrial septal defect (VATER association). Patients with SLPA, those with BB, or those with both SLPA and BB as well as multiple congenital anomalies represent a spectrum of anomalies.Entities:
Mesh:
Year: 1992 PMID: 1488977 DOI: 10.1002/ajmg.1320440308
Source DB: PubMed Journal: Am J Med Genet ISSN: 0148-7299