| Literature DB >> 14697961 |
A Bassas1, M Chehab, H Hebby, M Al Shahed, H Al Husseini, A Al Zahrani, S Wali.
Abstract
Progressive familial intrahepatic cholestasis (PFIC) is a heterogenous group of disorders with various etiologies. Recent molecular and genetic studies have categorized the spectrum of types. Liver transplantation is a curative modality of treatment in this disease. We report our experience with 13 patients with PFIC who underwent living related liver transplantation. The follow-up periods ranged from 12 to 50 months. Two children died at 1 and 2 years posttransplantation, leading to a decrease in survival rate from 100% in the first year to 84.6%.Entities:
Mesh：
Year: 2003 PMID： 14697961 DOI： 10.1016/j.transproceed.2003.10.047
Source DB: PubMed Journal: Transplant Proc ISSN： 0041-1345 Impact factor: 1.066