Acrokeratoelastoidosis associated with nodular scleroderma.

We report a case of acrokeratoelastoidosis associated with nodular scleroderma, a variant of localized scleroderma. The patient showed no clinical and laboratory signs of systemic scleroderma. Because there is a paper describing the association of acrokeratoelastoidosis with systemic scleroderma, coexistence of acrokeratoelastoidosis and nodular scleroderma in the patient suggests that acrokeratoelastoidosis is related to localized nodular scleroderma as well as systemic scleroderma.