Scimitar syndrome treated with pneumonectomy: a case associated with bronchospastic attack.

Scimitar syndrome, which involves total or partial anomalous venous drainage of the right lung to the inferior vena cava, is relatively rare and often results in pulmonary hypertension, heart failure and right lung infection. We report here the case of a 1-year-old girl who suffered repeated attacks of bronchospasm after developing pneumonia. She underwent resection of the hypoplastic right lung and showed rapid recovery.