Brad D Dresher1, Marc A Asher. 1. Section of Orthopedic Surgery, University of Kansas Medical Center, Kansas City, KS, USA.
Abstract
BACKGROUND CONTEXT: The management of early-onset progressive scoliosis is controversial. PURPOSE: To describe the unusual surgical management of a young female with an early-onset progressive, short, angular kyphoscoliosis resembling neurofibromatosis. STUDY DESIGN: A case report reviewing the treatment of an unusual occurrence of kyphoscoliosis. METHODS: After compliant Milwaukee brace wear had failed to stop deformity progression, surgical management including segmental anterior and posterior T5-T10 arthrodesis, and posterior T3-L4 subfascial rod instrumentation was performed at age 4 years and 6 months. After 10 rod lengthenings, segmental anterior T10 to L3 arthrodesis and posterior T3-L4 instrumentation and arthrodesis were done at age 11 years and 5 months. RESULTS: From preoperative to 3-year postoperative definitive surgery, her T3 to L4 instrumented spine length increased by 9.5 cm; 4 cm after the initial surgery, 3 cm between the initial surgery and the definitive surgery and 2.5 cm after the definitive surgery. From preoperative to latest follow-up, her thoracic scoliosis was reduced from 89 to 31 degrees, her thoracolumbar compensatory scoliosis from 59 to 37 degrees and her kyphosis from 70 to 17 degrees. CONCLUSIONS: The combination of early definitive anterior and posterior major curve arthrodesis with a subfascial rod lengthening program to control the remainder of the thoracolumbar spine was a satisfactory solution for this unusual case of early-onset, progressive, short, angular kyphoscoliosis.
BACKGROUND CONTEXT: The management of early-onset progressive scoliosis is controversial. PURPOSE: To describe the unusual surgical management of a young female with an early-onset progressive, short, angular kyphoscoliosis resembling neurofibromatosis. STUDY DESIGN: A case report reviewing the treatment of an unusual occurrence of kyphoscoliosis. METHODS: After compliant Milwaukee brace wear had failed to stop deformity progression, surgical management including segmental anterior and posterior T5-T10 arthrodesis, and posterior T3-L4 subfascial rod instrumentation was performed at age 4 years and 6 months. After 10 rod lengthenings, segmental anterior T10 to L3 arthrodesis and posterior T3-L4 instrumentation and arthrodesis were done at age 11 years and 5 months. RESULTS: From preoperative to 3-year postoperative definitive surgery, her T3 to L4 instrumented spine length increased by 9.5 cm; 4 cm after the initial surgery, 3 cm between the initial surgery and the definitive surgery and 2.5 cm after the definitive surgery. From preoperative to latest follow-up, her thoracic scoliosis was reduced from 89 to 31 degrees, her thoracolumbar compensatory scoliosis from 59 to 37 degrees and her kyphosis from 70 to 17 degrees. CONCLUSIONS: The combination of early definitive anterior and posterior major curve arthrodesis with a subfascial rod lengthening program to control the remainder of the thoracolumbar spine was a satisfactory solution for this unusual case of early-onset, progressive, short, angular kyphoscoliosis.