Literature DB >> 14316250

DEFICIENCIES OF -SH-DEPENDENT ENZYMES IN CYSTINOSIS.

A D PATRICK.   

Abstract

Keywords:  ALCOHOL OXIDOREDUCTASES; ALKALINE PHOSPHATASE; AMINOTRANSFERASES; CHILD; COENZYME A; CYSTEINE; CYSTINE; CYSTINOSIS; DIMERCAPROL; ENZYMES; GLUCOSEPHOSPHATASE; GLYCEROLPHOSPHATE DEHYDROGENASE; HEXOKINASE; HYDRO-LYASES; KIDNEY; LEUCINE AMINOPEPTIDASE; LIVER; MUSCLES; PENICILLAMINE; PHARMACOLOGY; PHOSPHOGLUCONATE DEHYDROGENASE; SUCCINATE DEHYDROGENASE; SULFHYDRYL COMPOUNDS; TISSUE EXTRACTS

Mesh:

Substances:

Year:  1965        PMID: 14316250

Source DB:  PubMed          Journal:  Clin Sci        ISSN: 0009-9287            Impact factor:   6.124


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  3 in total

1.  [Increase of beta-alanine in lymphocytes and thrombocytes for the biochemical diagnosis of cystinosis].

Authors:  G Wenske; F Linneweh
Journal:  Klin Wochenschr       Date:  1972-12-01

2.  Cysteamine prevents inhibition of thiol-containing enzymes caused by cystine or cystine dimethylester loading in rat brain cortex.

Authors:  Virginia Cielo Rech; Luciane Rosa Feksa; Rochele Marisa Müller Fleck; Genaro Azambuja Athaydes; Paula Karina Barcelos Dornelles; Valnes Rodrigues-Junior; Clovis Milton Duval Wannmacher
Journal:  Metab Brain Dis       Date:  2008-04-17       Impact factor: 3.584

3.  The redox status of cystinotic fibroblasts.

Authors:  Victor Vitvitsky; Marc Witcher; Ruma Banerjee; Jess Thoene
Journal:  Mol Genet Metab       Date:  2009-12-21       Impact factor: 4.797

  3 in total

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