Literature DB >> 1413496

Eccrine gland involvement in Krabbe's disease.

M Elleder1.   

Abstract

Lysosomal storage inclusions were observed in skin eccrine gland secretory and myoepithelial cells in three cases of Krabbe's disease. In addition to storage there were numerous degenerative changes, occasionally resulting in cell necrosis. These findings suggest a generalized nature of the storage process in this lysosomal enzymopathy and point to high galactocerebroside turnover in eccrine gland epithelium. This knowledge may be of value in the biopsy diagnosis of Krabbe's disease.

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Mesh：

Year:  1992        PMID： 1413496     DOI： 10.1007/bf01660983

Source DB:  PubMed          Journal:  Virchows Arch A Pathol Anat Histopathol        ISSN： 0174-7398


  11 in total

1.  A case of Krabbe's leukodystrophy without globoid cells.

Authors:  P McKelvie; P Vine; I Hopkins; A Poulos
Journal:  Pathology       Date:  1990-10       Impact factor: 5.306

2.  Occurrence of galactosylceramide in pig epidermal cells.

Authors:  S Hamanaka; Y Yamaguchi; T Yamamoto; C Asagami
Journal:  Biochim Biophys Acta       Date:  1988-08-12

3.  Further observations on the fine structure of globoid leukodystrophy. Peripheral neuropathy and optic nerve involvement.

Authors:  E J Yunis; R E Lee
Journal:  Hum Pathol       Date:  1972-09       Impact factor: 3.466

4.  Hepatic galactosylceramide in globoid cell leukodystrophy (Krabbe's disease).

Authors:  G Dawson
Journal:  Lipids       Date:  1973-03       Impact factor: 1.880

5.  Early infantile variant of Krabbe globoid cell leucodystrophy with lung involvement.

Authors:  J T Clarke; R L Ozere; V W Krause
Journal:  Arch Dis Child       Date:  1981-08       Impact factor: 3.791

6.  Characteristic inclusions in the kidney of canine globoid cell leukodystrophy.

Authors:  K Suzuki
Journal:  Acta Neuropathol       Date:  1986       Impact factor: 17.088

7.  [Sweat gland pathology in neurodegenerative disorders].

Authors:  S Kimura
Journal:  No To Hattatsu       Date:  1991-01

8.  Infantile and fetal globoid cell leukodystrophy: analysis of galactosylceramide and galactosylsphingosine.

Authors:  T Kobayashi; I Goto; T Yamanaka; Y Suzuki; T Nakano; K Suzuki
Journal:  Ann Neurol       Date:  1988-10       Impact factor: 10.422

9.  Murine globoid cell leukodystrophy (the twitcher mouse). The presence of characteristic inclusions in the kidney and lymph nodes.

Authors:  H Takahashi; H Igisu; K Suzuki; K Suzuki
Journal:  Am J Pathol       Date:  1983-08       Impact factor: 4.307

10.  Globoid cell leukodystrophy is a generalized galactosylsphingosine (psychosine) storage disease.

Authors:  T Kobayashi; H Shinoda; I Goto; T Yamanaka; Y Suzuki
Journal:  Biochem Biophys Res Commun       Date:  1987-04-14       Impact factor: 3.575
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