Literature DB >> 14089436

THE METABOLISM OF LEUCINE IN TISSUE CULTURE OF SKIN FIBROBLASTS OF MAPLE-SYRUP-URINE DISEASE.

J DANCIS, V JANSEN, J HUTZLER, M LEVITZ.   

Abstract

Keywords:  CARBON ISOTOPES; CARBOXY-LYASES; CONNECTIVE TISSUE; ENZYME TESTS; LEUCINE; MAPLE SYRUP URINE DISEASE; METABOLIC DISEASES; PROTEIN METABOLISM; SKIN; TISSUE CULTURE

Mesh：

Substances：

Year:  1963        PMID： 14089436     DOI： 10.1016/0006-3002(63)90536-5

Source DB:  PubMed          Journal:  Biochim Biophys Acta        ISSN： 0006-3002


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  7 in total

1.  Antenatal diagnosis of maple syrup urine disease.

Authors:  J J Hoo; E Latta; E Schaumlöffel
Journal:  Z Kinderheilkd       Date:  1974

2.  The absence of inactivation at two autosomal loci.

Authors:  B Sigman; S M Gartler
Journal:  Humangenetik       Date:  1966

3.  Mild variant of maple syrup urine disease.

Authors:  S Kodama; A Seki; M Hanabusa; Y Morisita; T Sakurai
Journal:  Eur J Pediatr       Date:  1976-12-09       Impact factor: 3.183

4.  Antibodies to bovine liver branched-chain 2-oxo acid dehydrogenase cross-react with this enzyme complex from other tissues and species.

Authors:  S C Heffelfinger; E T Sewell; D J Danner
Journal:  Biochem J       Date:  1983-08-01       Impact factor: 3.857

5.  Detection of heterozygotes in maple-syrup-urine disease: measurements of branched-chain alpha-ketoacid dehydrogenase and its components in cell cultures.

Authors:  D T Chuang; L S Ku; D S Kerr; R P Cox
Journal:  Am J Hum Genet       Date:  1982-05       Impact factor: 11.025

6.  Maple syrup urine disease: branched-chain amino acid concentrations and metabolism in cultured human lymphoblasts.

Authors:  S D Skaper; D P Molden; J E Seegmiller
Journal:  Biochem Genet       Date:  1976-08       Impact factor: 1.890

7.  Activities of branched-chain 2-oxo acid dehydrogenase and its components in skin fibroblasts from normal and classical-maple-syrup-urine-disease subjects.

Authors:  D T Chuang; W L Niu; R P Cox
Journal:  Biochem J       Date:  1981-10-15       Impact factor: 3.857
  7 in total

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