Literature DB >> 1309208

Hepatocellular carcinoma associated with arteriohepatic dysplasia in a 4-year-old girl.

A N Békássy1, S Garwicz, T Wiebe, I Hägerstrand, O A Jensen.   

Abstract

Hepatocellular carcinoma and obliterated hepatic bile duct were found at postmortem examination in a 4-year-old girl with arteriohepatic dysplasia (Alagille's syndrome). AFP level was extremely high. Liver cirrhosis was present on percutaneous needle biopsy 9 months before she succumbed in progressive liver failure. Episodes of repeated gastrointestinal, life-threatening hemorrhages occurred during the last 6 months of her life. Histopathologic findings of the eyes were documented at autopsy.

Entities:  

Mesh：

Year:  1992        PMID： 1309208     DOI： 10.1002/mpo.2950200118

Source DB:  PubMed          Journal:  Med Pediatr Oncol        ISSN： 0098-1532


  6 in total

1.  [Endocrinologic and metabolic complications of Alagille syndrome].

Authors:  L C Hofbauer; A Mrozek-Lasota; T Jelinek; H D Schworm; D Zimmermann; A E Heufelder
Journal:  Med Klin (Munich)       Date:  1997-09-15

2.  Outcome of liver disease in children with Alagille syndrome: a study of 163 patients.

Authors:  P Lykavieris; M Hadchouel; C Chardot; O Bernard
Journal:  Gut       Date:  2001-09       Impact factor: 23.059

3.  Management of large hepatocellular carcinoma in adult patients with Alagille syndrome: a case report and review of literature.

Authors:  Susan Tsai; Ahmet Gurakar; Robert Anders; Dora Lam-Himlin; John Boitnott; Timothy M Pawlik
Journal:  Dig Dis Sci       Date:  2010-01-27       Impact factor: 3.199

4.  Alagille Syndrome Candidates for Liver Transplantation: Differentiation from End-Stage Biliary Atresia Using Preoperative CT.

Authors:  Sook Min Hwang; Tae Yeon Jeon; So-Young Yoo; Ji Hye Kim; Ben Kang; Yon Ho Choe; Haeyon Cho; Jung Sun Kim
Journal:  PLoS One       Date:  2016-02-22       Impact factor: 3.240

5.  Alagille syndrome and risk for hepatocellular carcinoma: Need for increased surveillance in adults with mild liver phenotypes.

Authors:  Emma A Schindler; Melissa A Gilbert; David A Piccoli; Nancy B Spinner; Ian D Krantz; Kathleen M Loomes
Journal:  Am J Med Genet A       Date:  2020-12-24       Impact factor: 2.802

Review 6.  Genetics in Familial Intrahepatic Cholestasis: Clinical Patterns and Development of Liver and Biliary Cancers: A Review of the Literature.

Authors:  Giovanni Vitale; Alessandro Mattiaccio; Amalia Conti; Laura Turco; Marco Seri; Fabio Piscaglia; Maria Cristina Morelli
Journal:  Cancers (Basel)       Date:  2022-07-14       Impact factor: 6.575
  6 in total

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