Literature DB >> 12886142

Magnetic resonance imaging and spectroscopy in a patient with treated methylmalonic acidemia.

Mayumi Takeuchi1, Masafumi Harada, Kenji Matsuzaki, Sonoka Hisaoka, Hiromu Nishitani, Kenji Mori.   

Abstract

Magnetic resonance imaging (MRI) and proton magnetic resonance spectroscopy (proton MRS) findings before and after carnitine therapy in a patient with methylmalonic acidemia (MMA) are evaluated. The hyperintensity on T2-weighted image and diffusion-weighted image and the decreased apparent diffusion coefficient of bilateral basal ganglia were normalized in parallel with normalization of the elevated lactate levels and the decreased N-acetyl-aspartate levels, corresponding to improvement of clinical symptoms. MRI and proton MRS may serve as a suitable, noninvasive modality for monitoring treated MMA.

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Year:  2003        PMID： 12886142     DOI： 10.1097/00004728-200307000-00018

Source DB:  PubMed          Journal:  J Comput Assist Tomogr        ISSN： 0363-8715            Impact factor:   1.826


  10 in total

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  10 in total

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