Literature DB >> 12840537

Cystic fibrosis: premature degradation of mutant proteins as a molecular disease mechanism.

Marina S Gelman1, Ron R Kopito.   

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Year:  2003        PMID： 12840537     DOI： 10.1385/1-59259-394-1:27

Source DB:  PubMed          Journal:  Methods Mol Biol        ISSN： 1064-3745


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  8 in total

1.  Peroxisomal protein import and ERAD: variations on a common theme.

Authors:  Wolfgang Schliebs; Wolfgang Girzalsky; Ralf Erdmann
Journal:  Nat Rev Mol Cell Biol       Date:  2010-11-17       Impact factor: 94.444

Review 2.  Protein misfolding disorders: pathogenesis and intervention.

Authors:  N Gregersen
Journal:  J Inherit Metab Dis       Date:  2006 Apr-Jun       Impact factor: 4.982

3.  Der1 promotes movement of misfolded proteins through the endoplasmic reticulum membrane.

Authors:  Martin Mehnert; Thomas Sommer; Ernst Jarosch
Journal:  Nat Cell Biol       Date:  2013-12-01       Impact factor: 28.824

4.  Redundant and Antagonistic Roles of XTP3B and OS9 in Decoding Glycan and Non-glycan Degrons in ER-Associated Degradation.

Authors:  Annemieke T van der Goot; Margaret M P Pearce; Dara E Leto; Thomas A Shaler; Ron R Kopito
Journal:  Mol Cell       Date:  2018-04-26       Impact factor: 17.970

5.  NHE3 activity is dependent on direct phosphoinositide binding at the N terminus of its intracellular cytosolic region.

Authors:  Sachin Mohan; Chung Ming Tse; Sandra B Gabelli; Rafiquel Sarker; Boyoung Cha; Kamau Fahie; Mythili Nadella; Nicholas C Zachos; Becky Tu-Sekine; Daniel Raben; L Mario Amzel; Mark Donowitz
Journal:  J Biol Chem       Date:  2010-08-24       Impact factor: 5.157

6.  Chemical and biological folding contribute to temperature-sensitive DeltaF508 CFTR trafficking.

Authors:  Xiaodong Wang; Atanas V Koulov; Wendy A Kellner; John R Riordan; William E Balch
Journal:  Traffic       Date:  2008-07-30       Impact factor: 6.215

Review 7.  Lipids in the assembly of membrane proteins and organization of protein supercomplexes: implications for lipid-linked disorders.

Authors:  Mikhail Bogdanov; Eugenia Mileykovskaya; William Dowhan
Journal:  Subcell Biochem       Date:  2008

Review 8.  Sarcoglycanopathies: molecular pathogenesis and therapeutic prospects.

Authors:  Dorianna Sandonà; Romeo Betto
Journal:  Expert Rev Mol Med       Date:  2009-09-28       Impact factor: 5.600
  8 in total

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