Literature DB >> 12805338

Ovarian sex cord-stromal tumors in children and adolescents.

D T Schneider1, G Calaminus, R Wessalowski, R Pathmanathan, B Selle, W Sternschulte, D Harms, U Göbel, R Wessalowksi.   

Abstract

PURPOSE: To develop diagnostic standards and a risk-adapted therapeutic strategy for ovarian sex cord-stromal tumors (OSCST). PATIENTS AND METHODS: Fifty-four patients were prospectively enrolled as follow-up patients onto the German Maligne Keimzelltumoren protocols. Surgical protocols and histopathology were reviewed centrally (53 patients with complete data). Surgery included ovariectomy in 18 patients, salpingo-ovariectomy in 34 patients, and hysterectomy in one patient. Patients with stage IA tumors were followed-up at regular intervals, whereas nine patients with stage IC and six patients with stage II to III tumors were treated with cisplatin-based chemotherapy.
RESULTS: International Federation of Gynecology and Obstetrics stage was IA in 27 patients, IC in 21 patients, II in three patients, and III in three patients. After a median follow-up of 59 months (range, 6 to 193 months), event-free survival +/- SD was 0.86 +/- 0.05 (47 of 54 patients) and overall survival was 0.89 +/- 0.05 (49 of 54 patients). Prognosis correlated with stage (event-free survival +/- SD: IA, 1.0 [27 of 27 patients]; IC, 0.76 +/- 0.09 [16 of 21 patients]; and II/III, 0.67 +/- 0.19 [four of six patients]; P =.02). Ten of 15 patients treated with chemotherapy, including four of six stage II to III patients, are alive after a median follow-up of 33 months.
CONCLUSION: On the basis of a standardized clinical and histopathologic assessment, risk-adapted therapeutic strategies for OSCST can be evaluated. Considering our experience, we would recommend that stage IA tumors be followed up at regular intervals, whereas we would recommend cisplatin-based chemotherapy in stage IC tumors with preoperative rupture or malignant ascites, especially those with high mitotic activity. Finally, cisplatin-based chemotherapy also seems to be effective in advanced-stage tumors.

Entities:  

Mesh:

Year:  2003        PMID: 12805338     DOI: 10.1200/JCO.2003.05.038

Source DB:  PubMed          Journal:  J Clin Oncol        ISSN: 0732-183X            Impact factor:   44.544


  15 in total

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Authors:  Christopher Z Lam; Govind B Chavhan
Journal:  Pediatr Radiol       Date:  2018-08-04

2.  Ovarian Sex Cord-Stromal Tumors.

Authors:  Kris Ann P Schultz; Anne K Harris; Dominik T Schneider; Robert H Young; Jubilee Brown; David M Gershenson; Louis P Dehner; D Ashley Hill; Yoav H Messinger; A Lindsay Frazier
Journal:  J Oncol Pract       Date:  2016-10       Impact factor: 3.840

3.  DICER1-related Sertoli-Leydig cell tumor and gynandroblastoma: Clinical and genetic findings from the International Ovarian and Testicular Stromal Tumor Registry.

Authors:  Kris Ann P Schultz; Anne K Harris; Michael Finch; Louis P Dehner; Jubilee B Brown; David M Gershenson; Robert H Young; Amanda Field; Weiying Yu; Joyce Turner; Nicholas G Cost; Dominik T Schneider; Douglas R Stewart; A Lindsay Frazier; Yoav Messinger; D Ashley Hill
Journal:  Gynecol Oncol       Date:  2017-10-14       Impact factor: 5.482

4.  Ovarian sex cord-stromal tumors, pleuropulmonary blastoma and DICER1 mutations: a report from the International Pleuropulmonary Blastoma Registry.

Authors:  Kris Ann P Schultz; M Cristina Pacheco; Jiandong Yang; Gretchen M Williams; Yoav Messinger; D Ashley Hill; Louis P Dehner; John R Priest
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Journal:  Pediatr Radiol       Date:  2019-10-16

8.  Clinicopathologic characteristics of granulosa cell tumors of the ovary: a multicenter retrospective study.

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Journal:  J Gynecol Oncol       Date:  2011-09-28       Impact factor: 4.401

9.  Treatment of high risk Sertoli-Leydig cell tumors of the ovary using a gonadotropin releasing hormone (GnRH) analog.

Authors:  Harsha Prasada Lashkari; Ruth Nash; Assunta Albanese; Bruce Okoye; Robert Millar; Kathy Pritchard-Jones
Journal:  Pediatr Blood Cancer       Date:  2012-11-28       Impact factor: 3.167

10.  DICER1 hotspot mutations in non-epithelial gonadal tumours.

Authors:  L Witkowski; J Mattina; S Schönberger; M J Murray; C S Choong; D G Huntsman; J S Reis-Filho; W G McCluggage; J C Nicholson; N Coleman; G Calaminus; D T Schneider; J Arseneau; C J R Stewart; W D Foulkes
Journal:  Br J Cancer       Date:  2013-10-17       Impact factor: 7.640

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