Literature DB >> 12684896

Dilated cardiomyopathy in a 3-year-old girl with a terminal deletion, 46,XX,del(3)(q27-qter), of the long arm of chromosome 3.

Hideaki Senzaki1, Mika Inui, Shin-Ichi Ban, Satoshi Masutani, Mofeed Morsy, Toshiki Kobayashi, Hironori Nagasaka, Nozomu Sasaki, Shunei Kyo, Yuji Yokote.   

Abstract

UNLABELLED: We report a case in which a 3-year-old girl with terminal deletion of the long arm of chromosome 3 had dilated cardiomyopathy, a complication that has not previously been reported in association with this chromosome abnormality. In addition to cardiomyopathy, she had intrauterine growth retardation, small eyes and mouth, a broad nose, thin lips, low-set ears, a short neck and overlapping second toes.
CONCLUSION: due to the paucity of reported cases of 3q deletion, and the clinical variability of such cases, identification of a distinct 3q phenotype (including cardiac complications) remains elusive.

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Year:  2003        PMID: 12684896     DOI: 10.1007/s00431-003-1160-8

Source DB:  PubMed          Journal:  Eur J Pediatr        ISSN: 0340-6199            Impact factor:   3.183


  7 in total

Review 1.  Terminal deletion of the long arm of chromosome 3 [46,XX,del(3)(q27-->qter)].

Authors:  D Chitayat; R Babul; M M Silver; V Jay; I E Teshima; P Babyn; L E Becker
Journal:  Am J Med Genet       Date:  1996-01-02

Review 2.  Partial monosomy 3q in a boy with short stature, developmental delay, and mild dysmorphic features.

Authors:  L A Brueton; J C Barber; S M Huson; R M Winter
Journal:  J Med Genet       Date:  1989-11       Impact factor: 6.318

3.  Myocarditis: the Dallas criteria.

Authors:  H T Aretz
Journal:  Hum Pathol       Date:  1987-06       Impact factor: 3.466

4.  Report of the 1995 World Health Organization/International Society and Federation of Cardiology Task Force on the Definition and Classification of cardiomyopathies.

Authors:  P Richardson; W McKenna; M Bristow; B Maisch; B Mautner; J O'Connell; E Olsen; G Thiene; J Goodwin; I Gyarfas; I Martin; P Nordet
Journal:  Circulation       Date:  1996-03-01       Impact factor: 29.690

5.  Trigonocephaly and the Opitz C syndrome.

Authors:  C Sargent; J Burn; M Baraitser; M E Pembrey
Journal:  J Med Genet       Date:  1985-02       Impact factor: 6.318

6.  De novo del(3)(q2800).

Authors:  M C Alvarez Arratia; H Rivera; M Möller; A Valdivia; A Vigueras; J M Cantu
Journal:  Ann Genet       Date:  1984

7.  Deletion 3q27----3qter in an infant with mild dysmorphism, parietal meningocele, and neonatal miliaria rubra-like lesions.

Authors:  I Jokiaho; A Salo; K M Niemi; G C Blomstedt; J Pihkala
Journal:  Hum Genet       Date:  1989-10       Impact factor: 4.132

  7 in total
  2 in total

1.  The 3q29 microdeletion syndrome: report of three new unrelated patients and in silico "RNA binding" analysis of the 3q29 region.

Authors:  Majed J Dasouki; Gerald H Lushington; Karine Hovanes; James Casey; Mereceds Gorre
Journal:  Am J Med Genet A       Date:  2011-05-27       Impact factor: 2.802

Review 2.  Regulation of skin aging and heart development by TAp63.

Authors:  M Paris; M Rouleau; M Pucéat; D Aberdam
Journal:  Cell Death Differ       Date:  2011-12-09       Impact factor: 15.828

  2 in total

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