Literature DB >> 12541080

Characteristics of hydrocephalus expression in the LEW/Jms rat strain with inherited disease.

Hazel C Jones1, Barbara J Carter, Laurence Morel.   

Abstract

MATERIALS AND METHODS: The expression and severity of hydrocephalus was characterized in LEW/Jms rats with inherited hydrocephalus.
RESULTS: The frequency of overt disease (lethal) was 27.7%, but varied depending on breeding line. It increased to 31.5% when rats with mild disease were included. Most breeding pairs (48/51) produced hydrocephalic offspring with significantly more males than females affected. Some adult rats were also found to have mild (nonlethal) ventricular dilatation. When bred to Fisher F344 rats, 3% of the F(1) progeny had overt hydrocephalus, indicating that the trait is not recessive. Overt hydrocephalus was 9-20% in N(2) rats (F(1) rats x LEW/Jms). The frequency of hydrocephalus and the presence of an excess of hydrocephalic males, varied depending on the direction of the cross. Mild hydrocephalus in N(2) rats was 3.1%.
CONCLUSION: It is concluded that the inheritance of hydrocephalus in LEW/Jms strain is probably not mendelian recessive but may be semidominant or involve more than one gene and has a male bias indicating possible linkage to sex chromosomes.

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Year:  2002        PMID: 12541080     DOI: 10.1007/s00381-002-0671-3

Source DB:  PubMed          Journal:  Childs Nerv Syst        ISSN: 0256-7040            Impact factor:   1.475


  4 in total

1.  Clinical and neuropathological evolution of the hydrocephalus developed by the mutant mouse hyh.

Authors: 
Journal:  Cerebrospinal Fluid Res       Date:  2005-12-30

Review 2.  Genetics of human hydrocephalus.

Authors:  Jun Zhang; Michael A Williams; Daniele Rigamonti
Journal:  J Neurol       Date:  2006-06-13       Impact factor: 4.849

3.  Genetic loci for ventricular dilatation in the LEW/Jms rat with fetal-onset hydrocephalus are influenced by gender and genetic background.

Authors:  Hazel C Jones; Crystal F Totten; David A Mayorga; Mei Yue; Barbara J Carter
Journal:  Cerebrospinal Fluid Res       Date:  2005-06-12

Review 4.  Molecular Mechanisms and Risk Factors for the Pathogenesis of Hydrocephalus.

Authors:  Jingwen Li; Xinjie Zhang; Jian Guo; Chen Yu; Jun Yang
Journal:  Front Genet       Date:  2022-01-03       Impact factor: 4.599

  4 in total

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