Literature DB >> 12529774

[Anterior sacral meningocele with Currarino's syndrome: report of two cases].

J Dios Seoane1, S Amaro, M G Fantini, A Blanco, L López, A Rodiño, E Rossi, A Vázquez, J Díaz, V Goyanes, V Dios García.   

Abstract

The anterior sacral meningocele is the congenital hernia of the thecal sac into the pelvis through a bone defect of the anterior wall of the sacrum. The association of anorectal anomaly, anterior sacral defect and presacral mass, known as Currarino's triad, can be diagnosed during the first decade of life in the eighty per cent of the cases However, in the incomplete syndrome, the symptoms appear in adults. In order to avoid late complications and due to the clear genetic origin of this uncommon pathology, the investigation of the family is of paramount importance for the early diagnosis and treatment. We review the literature and add two cases of anterior sacral meningocele with rectal fistula and incomplete Currarino's syndrome. In one of the cases the pathology is also present in another member of the same family and is complicated with meningitis. The importance of early diagnosis and treatment of these malformations and the need for fammily genetic investigation are discussed.

Entities:  

Mesh:

Year:  2002        PMID: 12529774

Source DB:  PubMed          Journal:  Neurocirugia (Astur)        ISSN: 1130-1473            Impact factor:   0.553


  1 in total

1.  Lumbar puncture as a cause of tension pneumocephalus, pneumorrachis, and sacral meningocele infection leading to death: An extremely rare case report.

Authors:  Farid Aassouani; Zaid Ennacery; Abdellatif Bensalah; Yahya Charifi; Diallo Mamadou; Nizar El Bouardi; Meryem Haloua; Moulay Youssef Alaoui Lamrani; Abdoulmalek Ousadden; Meryem Boubbou; Mustapha Maaroufi; Badreeddine Alami
Journal:  Radiol Case Rep       Date:  2022-09-17
  1 in total

北京卡尤迪生物科技股份有限公司 © 2022-2023.