| Literature DB >> 12525998 |
Karen A Fagan1, David B Badesch.
Abstract
Pulmonary arterial hypertension is a life threatening complication of several connective tissue diseases including scleroderma (both diffuse and limited scleroderma, or the CREST syndrome--calcinosis cutis, Raynaud's phenomenon, esophageal dysfunction, sclerodactyly, and telangectasia), systemic lupus erythomatosis (SLE), mixed connective tissue disease (MCTD), and less commonly, rheumatoid arthritis (RA) and dermatomyositis/polymyositis. This report reviews the occurrence of this complication, potential etiologies, clinical presentation, and treatment options. Copyright 2002, Elsevier Science (USA). All rights reserved.Entities:
Mesh:
Substances:
Year: 2002 PMID: 12525998 DOI: 10.1053/pcad.2002.129975
Source DB: PubMed Journal: Prog Cardiovasc Dis ISSN: 0033-0620 Impact factor: 8.194