Literature DB >> 12511151

Presentation of Degos syndrome as acute small-bowel perforation.

Francisco Miguel González Valverde1, Francisco Menarguez Pina, Jose Antonio Ruiz, Maria Jesus Gómez Ramos, Francisco Mauri Barbera, Paloma Luri Prieto, Jose Antonio García Marcilla, Jose Luis Vázquez Rojas.   

Abstract

Malignant atrophic papulosis is an uncommon vasculopathy affecting multiple systems and frequently associated with a poor prognosis. We describe a 56-year-old patient with this rare disorder whose death was the result of intestinal involvement. Clinical diagnostic features of malignant atrophic papulosis as well as the main therapeutic approaches suggested in the literature are presented herein.

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Year:  2003        PMID: 12511151     DOI: 10.1001/archsurg.138.1.57

Source DB:  PubMed          Journal:  Arch Surg        ISSN: 0004-0010


  6 in total

1.  Surgery for small bowel perforation in an Asian population: predictors of morbidity and mortality.

Authors:  Ker-Kan Tan; Shieh-Ling Bang; Richard Sim
Journal:  J Gastrointest Surg       Date:  2009-12-09       Impact factor: 3.452

2.  Lethal systemic degos disease with prominent cardio-pulmonary involvement.

Authors:  Yaghoobi Notash Ali; Mazoochy Hamed; Nikoo Azita
Journal:  Indian J Dermatol       Date:  2011 Sep-Oct       Impact factor: 1.494

3.  Degos disease - malignant atrophic papulosis or cutaneointestinal lethal syndrome: rarity of the disease.

Authors:  Eduardo Pirolla; Felipe Fregni; Irene K Miura; Antonio Carlos Misiara; Fernando Almeida; Esdras Zanoni
Journal:  Clin Exp Gastroenterol       Date:  2015-04-16

4.  Clinical and laboratory prognosticators of atrophic papulosis (Degos disease): a systematic review.

Authors:  Justin D Lu; Muskaan Sachdeva; Orli M Silverberg; David Croitoru; Rebecca Levy; Lee Shapiro
Journal:  Orphanet J Rare Dis       Date:  2021-05-06       Impact factor: 4.123

Review 5.  Gastrointestinal Kohlmeier-Degos disease: a narrative review.

Authors:  Samantha S Sattler; Cynthia M Magro; Lee Shapiro; Jamie F Merves; Rebecca Levy; Jesse Veenstra; Puraj Patel
Journal:  Orphanet J Rare Dis       Date:  2022-04-20       Impact factor: 4.303

Review 6.  Laparoscopy shows superiority over endoscopy for early detection of malignant atrophic papulosis gastrointestinal complications: a case report and review of literature.

Authors:  A E Toledo; L S Shapiro; J F Farrell; C M Magro; J Polito
Journal:  BMC Gastroenterol       Date:  2015-11-02       Impact factor: 3.067

  6 in total

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