Acute pulmonary hypertensive crisis after TAPVC repair treated with atrial septectomy with inflow occlusion. Total anomalous pulmonary venous connection.

Acute pulmonary hypertensive crisis is a fatal complication after obstructive TAPVC repair. An atrial septectomy or enlargement of a small ASD could be a lifesaving procedure in order to maintain cardiac output in severe cases. This procedure can be accomplished with inflow occlusion in patients with critical condition.