Literature DB >> 12223993

Adult Henoch-Schönlein purpura with glomerulonephritis and paroxysmal nocturnal haemoglobinuria: an uncommon association.

F Cozzi1, C Botsios, P Ostuni, P Sfriso, E Piva, P Marson, L Punzi, S Todesco.   

Abstract

Henoch-Schönlein purpura (HSP) is considered to be a small blood vessel systemic vasculitis. Numerous microorganisms have been implicated in triggering HSP. We describe an unusual case of HSP with glomerulonephritis and renal failure requiring haemodialysis in a young adult man who subsequently developed paroxysmal nocturnal haemoglobinuria (PNH) with several haemolytic episodes. Bacterial infections, especially those of the respiratory and urinary tract, might trigger both the diseases.

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Year:  2002        PMID: 12223993     DOI: 10.1007/s100670200109

Source DB:  PubMed          Journal:  Clin Rheumatol        ISSN: 0770-3198            Impact factor:   2.980


  3 in total

Review 1.  Urological Manifestations of Henoch-Schonlein Purpura: A Review.

Authors:  Amanda Dalpiaz; Richard Schwamb; Yimei Miao; Jacquelyn Gonka; Wayne Walzter; Sardar A Khan
Journal:  Curr Urol       Date:  2015-07-10

2.  The presence of CD55- and/or CD59-deficient erythrocytic populations in patients with rheumatic diseases reflects an immune-mediated bone-marrow derived phenomenon.

Authors:  John V Asimakopoulos; Evangelos Terpos; Loula Papageorgiou; Olga Kampouropoulou; Dimitris Christoulas; Anastasios Giakoumis; Michael Samarkos; George Vaiopoulos; Konstantinos Konstantopoulos; Maria K Angelopoulou; Theodoros P Vassilakopoulos; John Meletis
Journal:  Med Sci Monit       Date:  2014-01-27

Review 3.  Complement Inhibition Therapy and Dialytic Strategies in Paroxysmal Nocturnal Hemoglobinuria: The Nephrologist's Opinion.

Authors:  Guido Gembillo; Rossella Siligato; Valeria Cernaro; Domenico Santoro
Journal:  J Clin Med       Date:  2020-04-26       Impact factor: 4.241

  3 in total

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