Literature DB >> 12149765

Intractable diarrhea after liver transplantation for Byler's disease: successful treatment with bile adsorptive resin.

Hiroto Egawa1, Tohru Yorifuji, Ryo Sumazaki, Akihiko Kimura, Makoto Hasegawa, Koichi Tanaka.   

Abstract

Intractable diarrhea and prolonged growth retardation after liver transplantation for Byler's disease are serious complications limiting the ultimate outcome of liver transplantation for this disease. However, details of these complications have not been documented thoroughly. Six patients with Byler's disease developed intractable diarrhea after living donor liver transplantation. Because of high bile acid concentrations in stool, four patients were treated with bile acid adsorptive resin for bile acid diarrhea, and all showed improved bowel movements. Four of these patients who were followed up for 1 year registered a significant height gain. Also, the cause of postoperative diarrhea and growth retardation in patients with Byler's disease after liver transplantation is discussed.

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Year:  2002        PMID： 12149765     DOI： 10.1053/jlts.2002.34384

Source DB:  PubMed          Journal:  Liver Transpl        ISSN： 1527-6465            Impact factor:   5.799


  17 in total

1.  Differences in presentation and progression between severe FIC1 and BSEP deficiencies.

Authors:  Ludmila Pawlikowska; Sandra Strautnieks; Irena Jankowska; Piotr Czubkowski; Karan Emerick; Anthony Antoniou; Catherine Wanty; Bjorn Fischler; Emmanuel Jacquemin; Sami Wali; Samra Blanchard; Inge-Merete Nielsen; Billy Bourke; Shirley McQuaid; Florence Lacaille; Jane A Byrne; Albertien M van Eerde; Kaija-Leena Kolho; Leo Klomp; Roderick Houwen; Peter Bacchetti; Steven Lobritto; Vera Hupertz; Patricia McClean; Giorgina Mieli-Vergani; Benjamin Shneider; Antal Nemeth; Etienne Sokal; Nelson B Freimer; A S Knisely; Philip Rosenthal; Peter F Whitington; Joanna Pawlowska; Richard J Thompson; Laura N Bull
Journal:  J Hepatol       Date:  2010-04-13       Impact factor: 25.083

Review 2.  Liver transplantation and the management of progressive familial intrahepatic cholestasis in children.

Authors:  Ashley Mehl; Humberto Bohorquez; Maria-Stella Serrano; Gretchen Galliano; Trevor W Reichman
Journal:  World J Transplant       Date:  2016-06-24

3.  Progressive Familial Intrahepatic Cholestasis (PFIC) in Indian Children: Clinical Spectrum and Outcome.

Authors:  Sajan Agarwal; Bikrant Bihari Lal; Dinesh Rawat; Archana Rastogi; Kishore G S Bharathy; Seema Alam
Journal:  J Clin Exp Hepatol       Date:  2016-05-24

Review 4.  Progressive familial intrahepatic cholestasis.

Authors:  Anshu Srivastava
Journal:  J Clin Exp Hepatol       Date:  2013-11-23

5.  Living-donor liver transplantation for progressive familial intrahepatic cholestasis.

Authors:  Tomohide Hori; Hiroto Egawa; Aya Miyagawa-Hayashino; Tohru Yorifuji; Yukihide Yonekawa; Justin H Nguyen; Shinji Uemoto
Journal:  World J Surg       Date:  2011-02       Impact factor: 3.352

6.  Novel resequencing chip customized to diagnose mutations in patients with inherited syndromes of intrahepatic cholestasis.

Authors:  Cong Liu; Bruce J Aronow; Anil G Jegga; Ning Wang; Alex Miethke; Reena Mourya; Jorge A Bezerra
Journal:  Gastroenterology       Date:  2006-10-21       Impact factor: 22.682

7.  ATP8B1 mutations in British cases with intrahepatic cholestasis of pregnancy.

Authors:  R Müllenbach; A Bennett; N Tetlow; N Patel; G Hamilton; F Cheng; J Chambers; R Howard; S D Taylor-Robinson; C Williamson
Journal:  Gut       Date:  2005-06       Impact factor: 23.059

Review 8.  Genetics of familial intrahepatic cholestasis syndromes.

Authors:  S W C van Mil; R H J Houwen; L W J Klomp
Journal:  J Med Genet       Date:  2005-06       Impact factor: 6.318

9.  Biochemical characterization of P4-ATPase mutations identified in patients with progressive familial intrahepatic cholestasis.

Authors:  Alex Stone; Christopher Chau; Christian Eaton; Emily Foran; Mridu Kapur; Edward Prevatt; Nathan Belkin; David Kerr; Torvald Kohlin; Patrick Williamson
Journal:  J Biol Chem       Date:  2012-10-11       Impact factor: 5.157

10.  ATP8B1 is essential for maintaining normal hearing.

Authors:  Janneke M Stapelbroek; Theo A Peters; Denis H A van Beurden; Jo H A J Curfs; Anneke Joosten; Andy J Beynon; Bibian M van Leeuwen; Lieke M van der Velden; Laura Bull; Ronald P Oude Elferink; Bert A van Zanten; Leo W J Klomp; Roderick H J Houwen
Journal:  Proc Natl Acad Sci U S A       Date:  2009-05-28       Impact factor: 11.205
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