Literature DB >> 12127226

McCune-Albright syndrome: a case report and review of the literature.

William E Bolger1, Adam T Ross.   

Abstract

Nasal obstruction is one of the most common symptoms pediatric patients present to their physicians with. Usually this symptom is caused by allergic rhinitis or an upper respiratory infection, however, many conditions present with nasal obstruction. We present a 14-year-old patient with a rare cause of nasal obstruction, turbinate enlargement due to fibrous dysplasia, as diagnosed by CT scan and histopathologic analysis. Additionally, clinical history revealed precocious puberty, and a dermatologic exam revealed a café au lait macule, consistent with the McCune-Albright syndrome. This case illustrates the need to formulate a broad differential diagnosis and also consider the overall patient, not just the nasal cavity. The clinical presentation, diagnostic evaluation, long-term management plan and relevant literature are discussed.

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Year:  2002        PMID: 12127226     DOI: 10.1016/s0165-5876(02)00125-8

Source DB:  PubMed          Journal:  Int J Pediatr Otorhinolaryngol        ISSN: 0165-5876            Impact factor:   1.675


  3 in total

1.  Oral Alendronate Treatment for Severe Polyostotic Fibrous Dysplasia due to McCune-Albright Syndrome in a Child: A Case Report.

Authors:  Ana Luiza Andrade Aragão; Ivani Novato Silva
Journal:  Int J Pediatr Endocrinol       Date:  2010-09-21

Review 2.  Fibrous dysplasia of the inferior turbinate.

Authors:  Hyun Joo Park; Min-Sun Cho; Seung-Sin Lee
Journal:  Int J Clin Exp Pathol       Date:  2013-02-15

3.  Sinonasal disease in polyostotic fibrous dysplasia and McCune-Albright Syndrome.

Authors:  Timothy R DeKlotz; Hung Jeffrey Kim; Marilyn Kelly; Michael T Collins
Journal:  Laryngoscope       Date:  2013-02-26       Impact factor: 3.325

  3 in total

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