Literature DB >> 12057744

Spontaneous pregnancy in a patient who was homozygous for the Q106R mutation in the gonadotropin-releasing hormone receptor gene.

Didier Dewailly1, Anne Boucher, Christine Decanter, Jean Pierre Lagarde, Raymond Counis, Marie-Laure Kottler.   

Abstract

OBJECTIVE: To report the occurrence of a spontaneous pregnancy in a patient who was homozygous for the Q106R mutation in the GnRH receptor (GnRHR) gene.
DESIGN: Case report.
SETTING: Reproductive endocrinology unit of an academic medical center. PATIENT(S): A 27-year-old woman who initially presented with partial idiopathic hypogonadotropic hypogonadism and who achieved a spontaneous pregnancy 3 months after oral contraceptive pill (OCP) withdrawal. INTERVENTION(S): Blood sampling for hormonal and genetic investigations, transvaginal ultrasound. MAIN OUTCOME MEASURE(S): LH, FSH, E2, and betahCG serum levels. Ultrasound examination of the uterine cavity. RESULT(S): Three months after OCP withdrawal, the patient was amenorrheic. However, the betahCG serum level was 149 IU/L. Transvaginal ultrasound 2 weeks later revealed the presence of one intrauterine sac containing two embryos with cardiac activity. At 9 weeks of gestation, no cardiac activity was found. A curettage was then performed, and the pathological examination indicated the presence of chorionic villi. CONCLUSION(S): OCP withdrawal might have induced a transient situation with optimal endogenous pulsatile GnRH secretion, thus overriding the GnRH resistance induced by the partially inactivating Q106R GnRHR gene mutation and allowing ovulation to occur.

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Year:  2002        PMID: 12057744     DOI: 10.1016/s0015-0282(02)03102-3

Source DB:  PubMed          Journal:  Fertil Steril        ISSN: 0015-0282            Impact factor:   7.329


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