Literature DB >> 11924535

Plastic bronchitis in children with Fontan palliation: analogue to protein losing enteropathy?

B Stiller1, F Riedel, K Paul, F K H van Landeghem.   

Abstract

We studied a 6-year-old boy and a 2-year-old girl with bronchitis fibroplastica following Fontan operation. Large endobronchial casts of rubber-like consistency resulted in life-threatening pulmonary failure. In one patient symptoms improved after optimizing heart function with diuretics, and in the other a dramatic improvement with the resolution of the clinical symptoms and normalized serum albumin followed subcutaneous high-molecular-weight heparin treatment. The severe relapse after discontinuation of the heparin medication and the once more successful treatment with heparin suggest that in addition to optimizing heart function, high-molecular-weight heparin might be a therapeutic option for this poorly understood condition.

Entities:  

Mesh：

Substances：

Year:  2002        PMID： 11924535     DOI： 10.1007/s00246-001-0024-0

Source DB:  PubMed          Journal:  Pediatr Cardiol        ISSN： 0172-0643            Impact factor:   1.655


  14 in total

1.  Anti-thrombin activities of heparin. Effect of saccharide chain length on thrombin inhibition by heparin cofactor II and by antithrombin.

Authors:  B Bray; D A Lane; J M Freyssinet; G Pejler; U Lindahl
Journal:  Biochem J       Date:  1989-08-15       Impact factor: 3.857

2.  Protein-losing enteropathy after the Fontan operation: an international multicenter study. PLE study group.

Authors:  L Mertens; D J Hagler; U Sauer; J Somerville; M Gewillig
Journal:  J Thorac Cardiovasc Surg       Date:  1998-05       Impact factor: 5.209

3.  [Association of severe bronchial disease (bronchial casts, bronchiectasis) and partial abnormal pulmonary venous drainage in 2 children with Turner's syndrome].

Authors:  F Counil; L Ichay; S Guillaumont; R Dumas; M Voisin
Journal:  Arch Pediatr       Date:  1999-10       Impact factor: 1.180

4.  Bronchial casts associated with hilar lymphatic and pulmonary lymphoid abnormalities.

Authors:  J Wiggins; E Sheffield; P K Jeffery; D M Geddes; B Corrin
Journal:  Thorax       Date:  1989-03       Impact factor: 9.139

5.  Bronchial casts in children with cardiopathies: the role of pulmonary lymphatic abnormalities.

Authors:  J Languepin; P Scheinmann; B Mahut; M Le Bourgeois; F Jaubert; F Brunelle; D Sidi; J de Blic
Journal:  Pediatr Pulmonol       Date:  1999-11

6.  Fontan's operation complications.

Authors:  W Duncan; M Tyrrell; B Bharadwaj; D George
Journal:  Pediatr Cardiol       Date:  1993-01       Impact factor: 1.655

7.  Reversal of protein-losing enteropathy with heparin therapy in three patients with univentricular hearts and Fontan palliation.

Authors:  J P Donnelly; A Rosenthal; V P Castle; R D Holmes
Journal:  J Pediatr       Date:  1997-03       Impact factor: 4.406

8.  Heparin therapy and reversal of protein-losing enteropathy in a case with congenital heart disease.

Authors:  I Bendayán; J Casaldaliga; F Castelló; L Miró
Journal:  Pediatr Cardiol       Date:  2000 May-Jun       Impact factor: 1.655

9.  Bronchial casts in children.

Authors:  J Werkhaven; L D Holinger
Journal:  Ann Otol Rhinol Laryngol       Date:  1987 Jan-Feb       Impact factor: 1.547

Review 10.  Developmental disorders of the lymphatic system.

Authors:  R Greenlee; H Hoyme; M Witte; P Crowe; C Witte
Journal:  Lymphology       Date:  1993-12       Impact factor: 1.286
View more
  8 in total

Review 1.  Successful management of plastic bronchitis in a child post Fontan: case report and literature review.

Authors:  Paul Do; Inderpal Randhawa; Terry Chin; Kourosh Parsapour; Eliezer Nussbaum
Journal:  Lung       Date:  2012-03-20       Impact factor: 2.584

2.  Fenestration of the Fontan circuit as treatment for plastic bronchitis.

Authors:  J Wilson; J Russell; W Williams; L Benson
Journal:  Pediatr Cardiol       Date:  2005 Sep-Oct       Impact factor: 1.655

Review 3.  The Long-Term Management of Children and Adults with a Fontan Circulation: A Systematic Review and Survey of Current Practice in Australia and New Zealand.

Authors:  Ganesh K Gnanappa; David S Celermajer; Gary F Sholler; Tom Gentles; David Winlaw; Yves d'Udekem; Julian Ayer
Journal:  Pediatr Cardiol       Date:  2016-10-27       Impact factor: 1.655

4.  Pharmacotherapy challenges of Fontan-associated plastic bronchitis: a rare pediatric disease.

Authors:  Kristina Brooks; Regine L Caruthers; Kurt R Schumacher; Kathleen A Stringer
Journal:  Pharmacotherapy       Date:  2013-05-17       Impact factor: 4.705

5.  Evaluating failing Fontans for heart transplantation: predictors of death.

Authors:  Eric R Griffiths; Aditya K Kaza; Moritz C Wyler von Ballmoos; Hugo Loyola; Anne Marie Valente; Elizabeth D Blume; Pedro del Nido
Journal:  Ann Thorac Surg       Date:  2009-08       Impact factor: 4.330

6.  Resolution of plastic bronchitis with atrial pacing in a patient with fontan physiology.

Authors:  B J Barber; G H Burch; D Tripple; S Balaji
Journal:  Pediatr Cardiol       Date:  2003-10-13       Impact factor: 1.655

Review 7.  Decision-Making for Surgery in the Management of Patients with Univentricular Heart.

Authors:  Ryan Robert Davies; Christian Pizarro
Journal:  Front Pediatr       Date:  2015-07-27       Impact factor: 3.418

8.  Airway emergency during general anesthesia in a child with plastic bronchitis following Fontan surgery: a case report.

Authors:  Hirofumi Nakamoto; Satoru Kayama; Mae Harada; Takahiro Honjo; Kinuko Kubota; Shigehito Sawamura
Journal:  JA Clin Rep       Date:  2020-01-21
  8 in total

北京卡尤迪生物科技股份有限公司 © 2022-2023.