Literature DB >> 11729709

Clinical experience in anesthetic management for children with mucopolysaccharidoses: Report of ten cases.

Y L Chan1, S P Lin, T T Man, C R Cheng.   

Abstract

The mucopolysaccharidoses (MPS) are hereditary disorders. Children with these disorders have multisystem disease and present significant challenges for the anesthesiologist. The establishment and maintenance of an adequate airway represents the most commonly encountered anesthesia-related problem in these patients. We report ten children with MPS who required surgical intervention. One patient died and the others had a good outcome. In this report, we share our experience and discuss the anesthetic risks and management of MPS patients.

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Year:  2001        PMID: 11729709

Source DB:  PubMed          Journal:  Acta Paediatr Taiwan        ISSN: 1608-8115


  6 in total

1.  Mucopolysaccharidosis I under enzyme replacement therapy with laronidase--a mortality case with autopsy report.

Authors:  H-Y Lin; S-P Lin; C-K Chuang; M-R Chen; B-F Chen; J E Wraith
Journal:  J Inherit Metab Dis       Date:  2005       Impact factor: 4.982

Review 2.  Mucopolysaccharidosis VI.

Authors:  Vassili Valayannopoulos; Helen Nicely; Paul Harmatz; Sean Turbeville
Journal:  Orphanet J Rare Dis       Date:  2010-04-12       Impact factor: 4.123

3.  Airway-related symptoms and surgeries in patients with mucopolysaccharidosis I.

Authors:  Pamela Arn; Iain A Bruce; James E Wraith; Helen Travers; Shari Fallet
Journal:  Ann Otol Rhinol Laryngol       Date:  2014-09-11       Impact factor: 1.547

4.  Management of difficult airway with laryngeal mask in a child with mucopolysaccharidosis and mitral regurgitation: a case report.

Authors:  Mohsen Ziyaeifard; Rasoul Azarfarin; Rasoul Ferasatkish; Majid Dashti
Journal:  Res Cardiovasc Med       Date:  2014-04-01

5.  The Anesthetic Strategy for Patients with Mucopolysaccharidoses: A Retrospective Cohort Study.

Authors:  Hsuan-Chih Lao; Ying-Chun Lin; Muh-Lii Liang; Ying-Wei Yang; Ya-Hsien Huang; Ying-Lun Chan; Yung-Wei Hsu; Shuan-Pei Lin; Chih-Kuang Chuang; Jen-Kun Cheng; Hsiang-Yu Lin
Journal:  J Pers Med       Date:  2022-08-21

6.  Otorhinolaryngological Management in Taiwanese Patients with Mucopolysaccharidoses.

Authors:  Chung-Lin Lee; Kuo-Sheng Lee; Chih-Kuang Chuang; Chin-Hui Su; Huei-Ching Chiu; Ru-Yi Tu; Yun-Ting Lo; Ya-Hui Chang; Hsiang-Yu Lin; Shuan-Pei Lin
Journal:  Int J Med Sci       Date:  2021-07-25       Impact factor: 3.738

  6 in total

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