Literature DB >> 11565695

Chylothorax complicating Gorham's disease.

N Chavanis1, P Chaffanjon, G Frey, G Vottero, P Y Brichon.   

Abstract

Gorham's disease is a rare disorder characterized by a proliferation of thin-walled lymphatic vessels (lymphangiectasia) resulting in an osteolysis. A chylothorax is present in about one-fifth of the patients and carries a poor prognosis. In this circumstance, surgery including thoracic duct ligation, pleurodesis, and excision of involved tissue is probably the treatment of choice. It is facilitated by a precise radiological assessment using a computed tomographic scanning coupled with a lymphography. We report such a case.

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Year:  2001        PMID: 11565695     DOI: 10.1016/s0003-4975(00)02417-6

Source DB:  PubMed          Journal:  Ann Thorac Surg        ISSN: 0003-4975            Impact factor:   4.330


  12 in total

1.  Efficacy of systemic sirolimus in the treatment of generalized lymphatic anomaly and Gorham-Stout disease.

Authors:  Kiersten W Ricci; Adrienne M Hammill; Paula Mobberley-Schuman; Stephen C Nelson; Julie Blatt; Julia L Glade Bender; Catherine C McCuaig; Anna Synakiewicz; Ilona J Frieden; Denise M Adams
Journal:  Pediatr Blood Cancer       Date:  2019-01-22       Impact factor: 3.167

Review 2.  Gorham's disease or massive osteolysis.

Authors:  Dipak V Patel
Journal:  Clin Med Res       Date:  2005-05

Review 3.  Novel molecular pathways in Gorham disease: implications for treatment.

Authors:  Jeroen Hagendoorn; Torunn I Yock; Inne H M Borel Rinkes; Timothy P Padera; David H Ebb
Journal:  Pediatr Blood Cancer       Date:  2013-11-08       Impact factor: 3.167

4.  Gorham-Stout disease and generalized lymphatic anomaly--clinical, radiologic, and histologic differentiation.

Authors:  Shailee Lala; John B Mulliken; Ahmad I Alomari; Steven J Fishman; Harry P Kozakewich; Gulraiz Chaudry
Journal:  Skeletal Radiol       Date:  2013-01-31       Impact factor: 2.199

5.  Mediastinal lymphangioma and chylothorax: thoracic involvement of Gorham's disease.

Authors:  So Young Yoo; Jin Mo Goo; Jung Gi Im
Journal:  Korean J Radiol       Date:  2002 Apr-Jun       Impact factor: 3.500

6.  Japanese clinical practice guidelines for vascular anomalies 2017.

Authors:  Hidefumi Mimura; Sadanori Akita; Akihiro Fujino; Masatoshi Jinnin; Mine Ozaki; Keigo Osuga; Hiroki Nakaoka; Eiichi Morii; Akira Kuramochi; Yoko Aoki; Yasunori Arai; Noriko Aramaki; Masanori Inoue; Yuki Iwashina; Tadashi Iwanaka; Shigeru Ueno; Akihiro Umezawa; Michio Ozeki; Junko Ochi; Yoshiaki Kinoshita; Masakazu Kurita; Shien Seike; Nobuyuki Takakura; Masataka Takahashi; Takao Tachibana; Kumiko Chuman; Shuji Nagata; Mitsunaga Narushima; Yasunari Niimi; Shunsuke Nosaka; Taiki Nozaki; Kazuki Hashimoto; Ayato Hayashi; Satoshi Hirakawa; Atsuko Fujikawa; Yumiko Hori; Kentaro Matsuoka; Hideki Mori; Yuki Yamamoto; Shunsuke Yuzuriha; Naoaki Rikihisa; Shoji Watanabe; Shinichi Watanabe; Tatsuo Kuroda; Shunsuke Sugawara; Kosuke Ishikawa; Satoru Sasaki
Journal:  Jpn J Radiol       Date:  2020-04       Impact factor: 2.374

7.  Japanese Clinical Practice Guidelines for Vascular Anomalies 2017.

Authors:  Hidefumi Mimura; Sadanori Akita; Akihiro Fujino; Masatoshi Jinnin; Mine Ozaki; Keigo Osuga; Hiroki Nakaoka; Eiichi Morii; Akira Kuramochi; Yoko Aoki; Yasunori Arai; Noriko Aramaki; Masanori Inoue; Yuki Iwashina; Tadashi Iwanaka; Shigeru Ueno; Akihiro Umezawa; Michio Ozeki; Junko Ochi; Yoshiaki Kinoshita; Masakazu Kurita; Shien Seike; Nobuyuki Takakura; Masataka Takahashi; Takao Tachibana; Kumiko Chuman; Shuji Nagata; Mitsunaga Narushima; Yasunari Niimi; Shunsuke Nosaka; Taiki Nozaki; Kazuki Hashimoto; Ayato Hayashi; Satoshi Hirakawa; Atsuko Fujikawa; Yumiko Hori; Kentaro Matsuoka; Hideki Mori; Yuki Yamamoto; Shunsuke Yuzuriha; Naoaki Rikihisa; Shoji Watanabe; Shinichi Watanabe; Tatsuo Kuroda; Shunsuke Sugawara; Kosuke Ishikawa; Satoru Sasaki
Journal:  J Dermatol       Date:  2020-03-22       Impact factor: 4.005

8.  Pleural Effusion in Spinal Deformity Correction Surgery- A Report of 28 Cases in a Single Center.

Authors:  Weiqiang Liang; Bin Yu; Yipeng Wang; Guixing Qiu; Jianxiong Shen; Jianguo Zhang; Hong Zhao; Yu Zhao; Ye Tian; Shugang Li
Journal:  PLoS One       Date:  2016-05-11       Impact factor: 3.240

9.  Gorham's Disease With Chest Wall Involvement: A Case Report and a Review of the Literature.

Authors:  Abolghasem Daneshvar Kakhaki; Kian Khodadad; Saviz Pejhan; Shirin Karimi; Mehrdad Arab; Reza Saghebi; Mohammad Behgam Shadmehr; Roya Farzanegan
Journal:  Iran Red Crescent Med J       Date:  2014-11-17       Impact factor: 0.611

10.  GORHAM-STOUT SYNDROME: PHANTOM BONE DISEASE.

Authors:  Gabriel El-Kouba; Romilton de Araújo Santos; Paulo César Pilluski; Antonio Severo; Osvandré Lech
Journal:  Rev Bras Ortop       Date:  2015-11-16
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