Nevus sebaceous of Jadassohn.

The nevus sebaceous of Jadassohn is a little known entity to most otolaryngologists. Most of the reported cases have occurred on the face or scalp. The lesion is usually congenital. It is a hairless, yellowish-red plaque until puberty when it becomes verrucous and unsightly. Benign or malignant tumors frequently develop. Associated ocular and central nervous system defects are occasionally present. The treatment is full-thickness excision as early as is feasible for cosmetic purposes and to avert the potential development of benign or malignant tumors.