Late outcome after the Fontan procedure.

Relatively little data exist on intermediate to late functional status and survival of patients after Fontan procedures. The first 500 patients undergoing a Fontan procedure at Children's Hospital (Boston, MA) were reviewed and then followed. There were 31 late failures among 410 patients contacted, and probability of survival at 10 years was 71.4%. Most patients were in functional class I or II, and only rare patients developed protein-losing enteropathy. Atrial flutter had developed in 16% of patients. Continued follow-up of Fontan patients will be necessary indefinitely. Copyright 1998 by W.B. Saunders Company