[Anesthetic management of a patient with Crow-Fukase syndrome complicated with severe heart failure].

A 31-year-old man with Crow-Fukase syndrome was scheduled for orthopedic surgery of the right lower limb. Preoperative examination revealed severe heart failure due to cardiomyopathy. Anesthesia was maintained with sevoflurane and nitrous oxide in oxygen, and supplemental fentanyl combined with continuous epidural block. During surgery, we evaluated cardiac function using transesophageal echocardiography. To maintain his cardiac function, intravenous dopamine and dobtamine were administered continuously, and the surgery was performed successfully. We must take care of cardiac function during anesthetic management of a patient with this syndrome.