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Literature DB >> 11404243

Chaperoning the maturation of the cystic fibrosis transmembrane conductance regulator.

J L Brodsky.

Abstract

Entities: Gene

Mesh：

Substances：

Year: 2001 PMID： 11404243 DOI： 10.1152/ajplung.2001.281.1.L39

Source DB: PubMed Journal: Am J Physiol Lung Cell Mol Physiol ISSN： 1040-0605 Impact factor: 5.464

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Cited

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9 in total

1. The CFTR Corrector, VX-809 (Lumacaftor), Rescues ABCA4 Trafficking Mutants: a Potential Treatment for Stargardt Disease.

Authors: Qiangni Liu; Inna Sabirzhanova; Emily Anne Smith Bergbower; Murali Yanda; William G Guggino; Liudmila Cebotaru
Journal: Cell Physiol Biochem Date: 2019

Review 2. Use of yeast as a model system to investigate protein conformational diseases.

Authors: Christina M Coughlan; Jeffrey L Brodsky
Journal: Mol Biotechnol Date: 2005-06 Impact factor: 2.695

3. Phenanthrolines--a new class of CFTR chloride channel openers.

Authors: M Duszyk; L MacVinish; A W Cuthbert
Journal: Br J Pharmacol Date: 2001-10 Impact factor: 8.739

4. A soluble sulfogalactosyl ceramide mimic promotes Delta F508 CFTR escape from endoplasmic reticulum associated degradation.

Authors: Hyun-Joo Park; Murugesapillai Mylvaganum; Anne McPherson; Sheara W Fewell; Jeffrey L Brodsky; Clifford A Lingwood
Journal: Chem Biol Date: 2009-04-24

5. Chaperone displacement from mutant cystic fibrosis transmembrane conductance regulator restores its function in human airway epithelia.

Authors: Fei Sun; Zhibao Mi; Steven B Condliffe; Carol A Bertrand; Xiaoyan Gong; Xiaoli Lu; Ruilin Zhang; Joseph D Latoche; Joseph M Pilewski; Paul D Robbins; Raymond A Frizzell
Journal: FASEB J Date: 2008-06-12 Impact factor: 5.191

Chaperoning the maturation of the cystic fibrosis transmembrane conductance regulator.

1. The CFTR Corrector, VX-809 (Lumacaftor), Rescues ABCA4 Trafficking Mutants: a Potential Treatment for Stargardt Disease.

Review 2. Use of yeast as a model system to investigate protein conformational diseases.

3. Phenanthrolines--a new class of CFTR chloride channel openers.

4. A soluble sulfogalactosyl ceramide mimic promotes Delta F508 CFTR escape from endoplasmic reticulum associated degradation.

5. Chaperone displacement from mutant cystic fibrosis transmembrane conductance regulator restores its function in human airway epithelia.

6. Calpain inhibition promotes the rescue of F(508)del-CFTR in PBMC from cystic fibrosis patients.

7. COPII-dependent export of cystic fibrosis transmembrane conductance regulator from the ER uses a di-acidic exit code.

8. The PEST sequence does not contribute to the stability of the cystic fibrosis transmembrane conductance regulator.

Review 9. Revisiting CFTR Interactions: Old Partners and New Players.