Literature DB >> 11393578

Clinical, endocrinological and radiography features in a child with McCune-Albright syndrome and pituitary adenoma.

W Zumkeller1, A Jassoy, S Lebek, M Nagel.   

Abstract

McCune-Albright syndrome is a rare syndrome presenting with polyostotic dysplasia, cafe-au-lait spots and multiple endocrinopathies that is very often combined with precocious puberty. We examined the clinical, endocrinological and radiological features in a boy with McCune-Albright syndrome and pituitary adenoma. X-rays, magnetic resonance (MRI) scan, whole body scintigraphy, single photon emission computer tomography (SPECT) and 3D-reconstruction from bone SPECT was performed to evaluate clinical improvement after treatment with sandostatin and pamidronic acid. After a six-month period of treatment with sandostatin and pamidronate, bone scintigraphy revealed significantly reduced activity. Treatment with bromocriptine and methimazole led to normalization of prolactin and thyroid hormone levels. Mobility of the patient improved. A significant improvement as a result of treatment with sandostatin and pamidronic acid was found in this patient with generalized fibrous dysplasia. So far, this condition has been treated with pamidronate only in adults, but severely affected children also benefit from this treatment regimen.

Entities:  

Mesh:

Substances:

Year:  2001        PMID: 11393578     DOI: 10.1515/jpem.2001.14.5.553

Source DB:  PubMed          Journal:  J Pediatr Endocrinol Metab        ISSN: 0334-018X            Impact factor:   1.634


  4 in total

1.  Pamidronate in a girl with chronic renal insufficiency dependent on parenteral nutrition.

Authors:  Janet L Duke; Deborah P Jones; Noel K Frizzell; Russell W Chesney; Emily B Hak
Journal:  Pediatr Nephrol       Date:  2003-05-15       Impact factor: 3.714

Review 2.  Acromegaly and McCune-Albright syndrome.

Authors:  Sylvie Salenave; Alison M Boyce; Michael T Collins; Philippe Chanson
Journal:  J Clin Endocrinol Metab       Date:  2014-02-11       Impact factor: 5.958

3.  Use of Zoledronic Acid in Paediatric Craniofacial Fibrous Dysplasia.

Authors:  Chiara Di Pede; Sabrina Congedi; Sara Rossin; Antuan Divisic; Alesandra De Gregorio; Caterina Agosto; Igor Catalano; Alessandro Mazza; Leonardo Sartori; Stefano Masiero; Franca Benini
Journal:  Case Rep Pediatr       Date:  2016-09-22

Review 4.  Clinical Characteristics and Management of Patients With McCune-Albright Syndrome With GH Excess and Precocious Puberty: A Case Series and Literature Review.

Authors:  Xiao Zhai; Lian Duan; Yong Yao; Bing Xing; Kan Deng; Linjie Wang; Feng Feng; Zhiyong Liang; Hui You; Hongbo Yang; Lin Lu; Shi Chen; Renzhi Wang; Hui Pan; Huijuan Zhu
Journal:  Front Endocrinol (Lausanne)       Date:  2021-10-29       Impact factor: 5.555

  4 in total

北京卡尤迪生物科技股份有限公司 © 2022-2023.