A rare form of interrupted aortic arch.

We report the case of a newborn with DiGeorge syndrome and aortic atresia associated with a complex anomaly of the aortic arch, interpreted as interrupted aortic arch type C, a persistent right ventral aorta and an aberrant right innominate artery. At 8 months the child underwent Norwood palliation with interposition of an 8 mm PTFE tube between the pulmonary trunk and the descending aorta and of a 3.5 mm shunt between the junction of the right ventral aorta to the left carotid artery and the right pulmonary artery. At 11 months he had substitution of the PTFE tube and bidirectional cavopulmonary anastomosis; he is now waiting for biventricular correction.