Literature DB >> 1118595

Pulmonary lymphangiectasia demonstrated by lymphangiography in 2 patients with Noonan's syndrome.

H A Baltaxe, J G Lee, K H Ehlers, M A Engle.   

Abstract

Two cases of pulmonary lymphangiectasia associated with Noonan's syndrome are described. Chest films showed diffuse pulmonary intersitial infiltrates from infancy. Lymphangiograms demonstrated obstructive changes and collateral formation in the retroperitoneal, mediastinal, pulmonary, and cervical lymphatics and extensive opacification of the pulmonary and visceral pleural lymphatics. Possible mechanisms and causes of the lymphatic malformation are discussed.

Entities:  

Mesh：

Year:  1975        PMID： 1118595     DOI： 10.1148/115.1.149

Source DB:  PubMed          Journal:  Radiology        ISSN： 0033-8419            Impact factor:   11.105


  9 in total

1.  Lymphocutaneous fistula as a long-term complication of multiple central venous catheter placement.

Authors:  R P Scharff; M R Recto; E H Austin; S A Wilkerson
Journal:  Tex Heart Inst J       Date:  2000

2.  Noonan syndrome: clinical aspects and molecular pathogenesis.

Authors:  M Tartaglia; G Zampino; B D Gelb
Journal:  Mol Syndromol       Date:  2010-01-15

3.  Spontaneous chylothorax in Noonan's syndrome.

Authors:  E Fisher; E B Weiss; K Michals; I W DuBrow; A R Hastrieter; R Matalon
Journal:  Eur J Pediatr       Date:  1982-05       Impact factor: 3.183

4.  Lymphatic abnormalities in Noonan's syndrome.

Authors:  P Lanning; S Similä; I Suramo; T Paavilainen
Journal:  Pediatr Radiol       Date:  1978-06-19

5.  Imaging of central lymphatic abnormalities in Noonan syndrome.

Authors:  David M Biko; Breanne Reisen; Hansel J Otero; Chitra Ravishankar; Teresa Victoria; Andrew C Glatz; Jonathan J Rome; Yoav Dori
Journal:  Pediatr Radiol       Date:  2019-01-06

6.  MR lymphangiography of lymphatic abnormalities in children and adults with Noonan syndrome.

Authors:  C C Pieper; J Wagenpfeil; A Henkel; S Geiger; T Köster; K Hoss; J A Luetkens; C Hart; U I Attenberger; A Müller
Journal:  Sci Rep       Date:  2022-07-01       Impact factor: 4.996

Review 7.  Cell Fate Determination of Lymphatic Endothelial Cells.

Authors:  Young Jae Lee
Journal:  Int J Mol Sci       Date:  2020-07-06       Impact factor: 5.923

8.  Pathological MAPK activation-mediated lymphatic basement membrane disruption causes lymphangiectasia that is treatable with ravoxertinib.

Authors:  Harish P Janardhan; Karen Dresser; Lloyd Hutchinson; Chinmay M Trivedi
Journal:  JCI Insight       Date:  2022-09-08

9.  KRAS-driven model of Gorham-Stout disease effectively treated with trametinib.

Authors:  Nassim Homayun-Sepehr; Anna L McCarter; Raphaël Helaers; Christine Galant; Laurence M Boon; Pascal Brouillard; Miikka Vikkula; Michael T Dellinger
Journal:  JCI Insight       Date:  2021-08-09
  9 in total

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